Motor Neuron DiseaseMotor NeuronsMuscular Atrophy, SpinalNeuromuscular DiseasesBulbar Palsy, ProgressiveSpinal Muscular Atrophies of ChildhoodAmyotrophic Lateral SclerosisSurvival of Motor Neuron 1 ProteinSpinal CordSMN Complex ProteinsSurvival of Motor Neuron 2 ProteinNeuronsMuscular AtrophyAtrophyAnterior Horn CellsMuscular Disorders, AtrophicBulbo-Spinal Atrophy, X-LinkedNerve DegenerationSuperoxide DismutaseFasciculationAxonsMotor CortexGaggingNeurons, AfferentElectromyographyTDP-43 ProteinopathiesNerve Tissue ProteinsNeurofilament ProteinsSpinal Cord DiseasesFrontotemporal Lobar DegenerationDEAD Box Protein 20Frontotemporal DementiaNeural ConductionDisease Models, AnimalInclusion BodiesMice, TransgenicEvoked Potentials, MotorToxascariasisbeta-Hexosaminidase beta ChainMotor ActivityRNA-Binding Protein FUSRiluzolePharyngostomyPyrrolidonecarboxylic AcidElectric InjuriesDeglutition DisordersMutationPick Disease of the BrainUlnar NerveNeuromuscular JunctionBrain Injury, ChronicRNA-Binding ProteinsBrainSpinal Cord InjuriesLathyrismPeripheral NervesCyclic AMP Response Element-Binding ProteinAction PotentialsMuscle, SkeletalSpinal Nerve RootsNeuronal Apoptosis-Inhibitory ProteinSandhoff DiseaseNeurologic ExaminationMarchiafava-Bignami DiseaseRats, TransgenicAxonal TransportCricoid CartilageDementiaMuscle WeaknessParalysisDNA Repeat ExpansionElectric StimulationPedigreeAge of OnsetMusclesRecruitment, NeurophysiologicalImmunohistochemistryPhenotypeAnimals, Genetically ModifiedCells, CulturedTime FactorsSpastic Paraplegia, HereditaryMice, Inbred C57BLGastrostomyReceptors, AndrogenCell DeathSynapsesNervous System DiseasesMutation, MissenseNeuroprotective AgentsCell CountMolecular Motor ProteinsGanglia, SpinalMice, KnockoutRibonucleoproteins, Small NuclearDisease ProgressionNeurodegenerative DiseasesThyrotropin-Releasing HormoneNeuroimagingInterneurons