Cystic FibrosisCystic Fibrosis Transmembrane Conductance RegulatorFibrosisPseudomonas InfectionsPseudomonas aeruginosaSweatSputumMice, Inbred CFTRBurkholderia InfectionsBurkholderia cepaciaChloridesEndomyocardial FibrosisIdiopathic Pulmonary FibrosisLungExocrine Pancreatic InsufficiencyLiver CirrhosisChloride ChannelsRespiratory MucosaTobramycinNasal MucosaPancreatinNeonatal ScreeningForced Expiratory VolumeRetroperitoneal FibrosisMutationBurkholderia cepacia complexRespiratory Function TestsPancreatic ExtractsRespiratory SystemBronchiectasisEpithelial CellsLung DiseasesNitrogenAnti-Bacterial AgentsBronchiLung TransplantationMucusHeterozygote DetectionAlginatesMeconiumExpectorantsDietBleomycinPancrelipaseNutritional StatusTracheaAchromobacter denitrificansPhenotypeDisease Models, AnimalMucociliary ClearanceBurkholderia cenocepaciaSweat GlandsCell LineIon TransportEnergy IntakeFoodAminophenolsTime FactorsMolecular Sequence DataNutritive ValueAspergillosis, Allergic BronchopulmonaryGenotypeLeukocyte ElastaseOral Submucous FibrosisNutritional Physiological PhenomenaVital CapacityCells, CulturedRespiratory Tract InfectionsEpitheliumLiver Cirrhosis, ExperimentalAmilorideHexuronic AcidsAdministration, InhalationGenetic TestingNutritional RequirementsGlucuronic AcidCulture MediaDrainage, PosturalAnimal Nutritional Physiological PhenomenaColistinChronic DiseaseMembrane ProteinsMice, Inbred C57BLStenotrophomonas maltophiliaInfant, NewbornRNA, MessengerMucinsHydroxyprolineBurkholderiaExocrine GlandsPolymerase Chain ReactionLiverCyclic AMPBronchoalveolar Lavage FluidPhosphorusColforsinRespiratory TherapyHepatic Stellate CellsSignal TransductionBicarbonates