Muscular Atrophy, SpinalSpinal Muscular Atrophies of ChildhoodSurvival of Motor Neuron 1 ProteinAtrophySMN Complex ProteinsMuscular AtrophySurvival of Motor Neuron 2 ProteinSpinal CordMuscular Disorders, AtrophicBulbo-Spinal Atrophy, X-LinkedSpinal Cord InjuriesNeuronal Apoptosis-Inhibitory ProteinCyclic AMP Response Element-Binding ProteinMotor NeuronsAnterior Horn CellsNerve Tissue ProteinsRNA-Binding ProteinsSpinal Cord DiseasesOptic AtrophyMotor Neuron DiseaseRibonucleoproteins, Small NuclearDisease Models, AnimalDEAD Box Protein 20NeuronsSpinal Nerve RootsInjections, SpinalChromosomes, Human, Pair 5ExonsSpinal NervesMultiple System AtrophyCoiled BodiesAnesthesia, SpinalNerve DegenerationMice, TransgenicReceptors, AndrogensnRNP Core ProteinsBrainAxonsSpinal Cord NeoplasmsSpinal CanalMuscle, SkeletalSpinal Cord CompressionSpinal DiseasesSpinal NeoplasmsPedigreePhenotypeMagnetic Resonance ImagingRats, Sprague-DawleyElectromyographyBulbar Palsy, ProgressiveSpinal StenosisMutationSpinal FusionCells, CulturedCharcot-Marie-Tooth DiseaseMuscle WeaknessHeterozygote DetectionNeural ConductionNeuronal PlasticityGanglia, SpinalOlivopontocerebellar AtrophiesContractureGene DeletionNeuromuscular DiseasesGlycine-tRNA LigaseArthrogryposisImmunohistochemistryHomozygoteNeuromuscular JunctionVocal Cord ParalysisHippocampusTime FactorsAmyotrophic Lateral SclerosisTrinucleotide Repeat ExpansionSpinal InjuriesMice, KnockoutNeuritesGyrate AtrophyAnimals, NewbornRNA SplicingMolecular Sequence DataMotor ActivityNeuromuscular Junction DiseasesMice, Inbred C57BLCerebral CortexSpinal Cord IschemiaInclusion BodiesAction PotentialsGenes, RecessiveIntranuclear Inclusion BodiesGene Expression RegulationGenetic LinkageGene DosageSural NerveNeurodegenerative DiseasesNeurofilament ProteinsTrinucleotide RepeatsGenes, DominantGeographic AtrophyNeuroprotective Agents