Neurodegenerative DiseasesMotor NeuronsNeuronsMotor Neuron DiseaseAmyotrophic Lateral SclerosisSurvival of Motor Neuron 1 ProteinNerve DegenerationNeurons, AfferentNerve Tissue ProteinsSurvival of Motor Neuron 2 ProteinSpinal CordBrainMotor CortexMuscular Atrophy, SpinalEvoked Potentials, MotorParkinson DiseaseMotor ActivityAlzheimer DiseaseDisease Models, Animaltau ProteinsAxonsHuntington DiseaseMice, Transgenicalpha-SynucleinNeuroprotective AgentsSMN Complex ProteinsInclusion BodiesCells, CulturedMutationSuperoxide DismutaseCell DeathTauopathiesMicrogliaAction PotentialsSynapsesDopaminergic NeuronsHeredodegenerative Disorders, Nervous SystemAxonal TransportCerebral CortexImmunohistochemistryHippocampusMice, Inbred C57BLProteostasis DeficienciesCentral Nervous SystemAstrocytesAnimals, Genetically ModifiedPrionsFrontotemporal Lobar DegenerationAmyloid beta-PeptidesOxidative StressSynucleinsPrion DiseasesSynaptic TransmissionFrontotemporal DementiaSpinocerebellar AtaxiasMitochondriaMolecular Motor ProteinsNeurogliaNeurofilament ProteinsElectric StimulationNeurotoxinsNeuromuscular DiseasesTime FactorsSignal TransductionCell SurvivalElectrophysiologyModels, BiologicalGanglia, InvertebrateTrinucleotide Repeat ExpansionAnimals, NewbornAgingDendritesNeuromuscular JunctionParkinsonian DisordersDopamineGreen Fluorescent ProteinsCerebellumGuamMice, KnockoutCholinergic NeuronsInterneuronsRNA-Binding Protein FUSBehavior, AnimalModels, NeurologicalGlutamic AcidNeurogenesisGene Expression RegulationRats, Sprague-DawleyAutophagySubstantia NigraFriedreich AtaxiaMovementGanglia, SpinalSensory Receptor CellsAnterior Horn CellsPatch-Clamp TechniquesRotarod Performance TestAnalysis of VarianceAplysiaCorpus Striatum