Neurodegenerative DiseasesAlzheimer Diseasetau ProteinsNerve DegenerationBrainAmyloid beta-PeptidesNeuronsAmyotrophic Lateral SclerosisParkinson DiseaseHuntington Diseasealpha-SynucleinNeurofibrillary TanglesTauopathiesNerve Tissue ProteinsDisease Models, AnimalNeuroprotective AgentsAmyloid beta-Protein PrecursorMice, TransgenicPlaque, AmyloidInclusion BodiesAmyloidHeredodegenerative Disorders, Nervous SystemMicrogliaDementiaPrionsProteostasis DeficienciesPrion DiseasesSynucleinsFrontotemporal Lobar DegenerationOxidative StressMutationFrontotemporal DementiaCell DeathAgingSpinocerebellar AtaxiasLewy Body DiseaseMitochondriaAtrophyTrinucleotide Repeat ExpansionCognition DisordersHippocampusAutophagyFriedreich AtaxiaAstrocytesCells, CulturedLewy BodiesCerebral CortexNeuronal Ceroid-LipofuscinosesGuamPeptidesPresenilin-1Protein FoldingModels, BiologicalNeurotoxinsNeuropsychological TestsNeurofibrilsApolipoprotein E4Mice, Inbred C57BLSuperoxide DismutasePeptide FragmentsParkinsonian DisordersMagnetic Resonance ImagingAmyloid Precursor Protein SecretasesSupranuclear Palsy, ProgressiveCentral Nervous SystemGliosisPick Disease of the BrainCentral Nervous System DiseasesAxonal TransportUbiquitinBrain ChemistryTrinucleotide RepeatsAmyloidogenic ProteinsImmunohistochemistrySignal TransductionMotor Neuron DiseaseProteasome Endopeptidase ComplexMitochondrial DiseasesMotor NeuronsGene Expression RegulationCell SurvivalDementia, VascularCycasIron-Binding ProteinsCyclin-Dependent Kinase 5NeurogliaApoptosisMolecular Sequence DataBlotting, WesternMuscular Atrophy, SpinalNervous System DiseasesAge of OnsetNeurofilament ProteinsPrPC ProteinsRNA-Binding Protein FUSReactive Oxygen SpeciesCell LineNuclear ProteinsMild Cognitive ImpairmentDNA Repeat Expansion