Motor NeuronsNeuronsMotor Neuron DiseaseCentral Nervous SystemSurvival of Motor Neuron 1 ProteinNeurons, AfferentNervous SystemSpinal CordMotor CortexSurvival of Motor Neuron 2 ProteinEvoked Potentials, MotorAmyotrophic Lateral SclerosisMotor ActivityMuscular Atrophy, SpinalAxonsNerve Tissue ProteinsSMN Complex ProteinsPeripheral Nervous SystemAction PotentialsBrainCentral Nervous System DiseasesGanglia, InvertebrateNerve DegenerationSynapsesElectric StimulationEnteric Nervous SystemMolecular Motor ProteinsNeuromuscular DiseasesCells, CulturedElectrophysiologySynaptic TransmissionMice, TransgenicImmunohistochemistryInterneuronsMovementAplysiaGanglia, SpinalSensory Receptor CellsCholinergic NeuronsElectromyographyNeuromuscular JunctionDendritesDisease Models, AnimalTime FactorsDopaminergic NeuronsSuperoxide DismutaseAnimals, NewbornModels, NeurologicalCerebral CortexGene Expression Regulation, DevelopmentalNeurogliaAnterior Horn CellsNervous System Physiological PhenomenaSympathetic Nervous SystemPatch-Clamp TechniquesNeural InhibitionNeuropeptidesAnimals, Genetically ModifiedCentral Nervous System NeoplasmsHippocampusGABAergic NeuronsBrain StemGangliaBulbar Palsy, ProgressiveMice, Inbred C57BLMutationAutonomic Nervous SystemPeripheral NervesMembrane PotentialsAstrocytesgamma-Aminobutyric AcidFacial NerveAxonal TransportRats, Sprague-DawleyBehavior, AnimalGrasshoppersNeurofilament ProteinsMotor Skills DisordersNeural ConductionNeuronal PlasticityIn Situ HybridizationGreen Fluorescent ProteinsLeechesNervous System DiseasesMice, KnockoutNerve NetCholine O-AcetyltransferaseLocomotionCell DifferentiationCerebellumNeurogenesisChick EmbryoNerve Growth FactorsGlutamic AcidNerve RegenerationMolecular Sequence DataCell CountMedulla OblongataNeurons, EfferentSignal Transduction