Diabetes Insipidus, NephrogenicNephrogenic Fibrosing DermopathyAquaporin 2Diabetes InsipidusReceptors, VasopressinGadoliniumAquaporin 6PolyuriaAquaporinsDeamino Arginine VasopressinRenal AgentsSkin DiseasesKidney Concentrating AbilityFanconi SyndromeContrast MediaInappropriate ADH SyndromeWilms TumorGadolinium DTPAKidneyArginine VasopressinKidney Tubules, CollectingPAX2 Transcription FactorNephronsWater DeprivationRenal InsufficiencyLithium CarbonateLithiumVasopressinsUreterSpectroscopy, Electron Energy-LossFibrosisFactor XIIIaAntidiuretic AgentsRenal AminoaciduriasGenes, Wilms TumorAquaporin 3Acidosis, Renal TubularKidney DiseasesMicroscopy, Energy-Filtering Transmission ElectronHydronephrosisThirstLithium CompoundsUrologic NeoplasmsRats, BrattleboroPseudopseudohypoparathyroidismKidney TubulesDiuresisThiosulfatesPedigreeUrineKidney Diseases, CysticUreteral NeoplasmsWater-Electrolyte ImbalanceKidney Failure, ChronicWater-Electrolyte BalanceX ChromosomeAquaporin 1MutationAdenomaOsmolar ConcentrationMesodermKidney MedullaKidney NeoplasmsWT1 ProteinsKeratin-7Organometallic CompoundsMagnetic Resonance AngiographyBone Morphogenetic Protein 7Frameshift MutationImmunohistochemistryGenes, RecessiveMutation, MissenseMagnetic Resonance ImagingOrganogenesisWaterSkinMolecular Sequence DataPoint MutationHeterocyclic CompoundsGene Expression Regulation, DevelopmentalPaired Box Transcription FactorsDNA Mutational AnalysisBase SequenceCyclic AMPBenzazepinesRenal DialysisIn Situ HybridizationEmbryonic and Fetal DevelopmentGlomerular Filtration RateProtein TransportHeterozygotePhenotypeMorphogenesisAmino Acid SequenceOocytes