Nasal MucosaCystic FibrosisCystic Fibrosis Transmembrane Conductance RegulatorEpitheliumFibrosisTurbinatesMice, Inbred CFTRNose DiseasesNoseMucociliary ClearanceOlfactory MucosaChloridesOlfactory NerveRespiratory MucosaRhinitisNasal CavityEpithelial CellsNasal PolypsCiliaAdministration, IntranasalAmilorideNasal SeptumPseudomonas InfectionsLungFormaldehydeIon TransportPseudomonas aeruginosaInhalation ExposureNasal Lavage FluidOzoneSweatSputumGene Transfer TechniquesCells, CulturedGenetic TherapyBurkholderia InfectionsBurkholderia cepaciaNasal DecongestantsEpithelium, CornealNasal BoneIdiopathic Pulmonary FibrosisEndomyocardial FibrosisGlycoproteinsRespiratory SystemChloride ChannelsBronchiExocrine Pancreatic InsufficiencyTracheaLiver CirrhosisNasal SpraysMucusTobramycinForced Expiratory VolumePancreatinNeonatal ScreeningMutationSeminiferous EpitheliumRespiratory Function TestsRetroperitoneal FibrosisNose NeoplasmsBurkholderia cepacia complexBronchiectasisLung DiseasesPancreatic ExtractsImmunohistochemistryRetinal Pigment EpitheliumAnti-Bacterial AgentsDisease Models, AnimalLung TransplantationNasal CartilagesRNA, MessengerCell LineExpectorantsSinusitisHeterozygote DetectionTime FactorsMice, Inbred C57BLMeconiumPhenotypeIntestinal MucosaAlginatesMucinsBleomycinSweat GlandsAdministration, InhalationPancrelipaseMolecular Sequence DataParanasal SinusesRespiratory Tract InfectionsExocrine GlandsAchromobacter denitrificansMembrane ProteinsNasal LavageBurkholderia cenocepaciaPolymerase Chain ReactionGene ExpressionVital CapacityGenotypeLeukocyte ElastaseOral Submucous Fibrosis