GlucokinasePoint MutationMutation, MissenseMutationHexokinaseFrameshift MutationGlucoseGerm-Line MutationMannoheptulosePedigreeLiverBase SequenceDihydroxyacetoneGlucose Transporter Type 2Islets of LangerhansNinhydrinMolecular Sequence DataExonsMutation RateHeterozygoteAmino Acid SubstitutionInsulinPolymerase Chain ReactionAmino Acid SequenceFructosephosphatesGlucose-6-PhosphateMutagenesis, Site-DirectedAllelesKineticsInsulinomaDNA Mutational AnalysisLiver GlycogenGenotypePolymorphism, Single-Stranded ConformationalHomozygoteSorbitolRNA, MessengerGlycolysisMutagenesisDNA PrimersSequence Analysis, DNAFructoseCodon, NonsenseGlucose-6-PhosphataseEscherichia coliCloning, MolecularGenetic TestingBinding SitesModels, MolecularCell LineGenes, RecessiveProtein Structure, TertiaryCarrier ProteinsSequence DeletionAdenoma, Islet CellPhenotypePyruvate KinaseGlucosephosphatesGene Expression Regulation, EnzymologicRats, WistarSequence Homology, Amino AcidCells, CulturedTranscription, GeneticPhosphofructokinase-2Protein BindingDNA-Binding ProteinsGenes, DominantChromosome MappingDNAPhosphoenolpyruvate Carboxykinase (GTP)Transcription FactorsSuppression, GeneticBlood GlucosePromoter Regions, GeneticRecombinant ProteinsGene ExpressionTransfectionCodonGlucagonSequence AlignmentDiabetes Mellitus, Type 2AlloxanSaccharomyces cerevisiaeProteinsGenetic Complementation TestPhosphorylationBacterial ProteinsGene DeletionGenetic Predisposition to DiseaseHexosesProtein ConformationMonosaccharide Transport ProteinsHepatocytesPolymorphism, GeneticHyperglycemiaEnzyme ActivatorsFounder EffectIntronsPlasmidsGenes