DystrophinMuscular Dystrophy, DuchenneMice, Inbred mdxUtrophinDystrophin-Associated ProteinsMuscular Dystrophy, AnimalMuscular DystrophiesMorpholinosExonsMuscle, SkeletalPoint MutationMutation, MissenseOligonucleotides, AntisenseMutationMuscle ProteinsGenetic TherapyFrameshift MutationMice, Inbred C57BLDystroglycansSarcolemmaGerm-Line MutationPedigreeMolecular Sequence DataSarcoglycansBase SequencePolymerase Chain ReactionCytoskeletal ProteinsAmino Acid SequenceHeterozygoteMutation RateSequence DeletionDNA Mutational AnalysisCodon, NonsenseMusclesAmino Acid SubstitutionMembrane ProteinsDystrophin-Associated Protein ComplexAllelesMuscle Fibers, SkeletalPolymorphism, Single-Stranded ConformationalPhenotypeGenotypeSequence Analysis, DNAMutagenesis, Site-DirectedMutagenesisProtein Structure, TertiaryOligoribonucleotides, AntisenseGenes, RecessiveHeterozygote DetectionDNA Primers