LamininBasement MembraneReceptors, LamininGlomerular Basement MembranePoint MutationAnti-Glomerular Basement Membrane DiseaseMutation, MissenseKidney GlomerulusMutationCollagen Type IVCell MembraneMembranesCollagenMembrane LipidsMicroscopy, ElectronIntracellular MembranesExtracellular MatrixMembrane PotentialsMembranes, ArtificialHeparan Sulfate ProteoglycansFluorescent Antibody TechniqueMolecular Sequence DataFrameshift MutationFibronectinsCell AdhesionAmino Acid SequenceNephritis, HereditaryBase SequenceMembrane GlycoproteinsCells, CulturedCell LineGlomerulonephritisHeparitin SulfateErythrocyte MembraneEpitheliumGerm-Line MutationMembrane FluidityDystroglycansProteoglycansImmunohistochemistryCell Membrane PermeabilityProtein BindingIntegrinsPedigreeProtein Structure, TertiaryKidneyCapillariesEpithelial CellsBinding SitesRNA, MessengerCell MovementExtracellular Matrix ProteinsDescemet MembraneElectrophoresis, Polyacrylamide GelExonsModels, BiologicalIntegrin alpha6beta1Polymerase Chain ReactionMicroscopy, FluorescenceMembrane Transport ProteinsEscherichia coliCarrier ProteinsChondroitin Sulfate ProteoglycansIntegrin alpha3beta1Molecular WeightHeterozygoteAmino Acid SubstitutionMutation RateGlycoproteinsAntibodiesBlotting, WesternModels, MolecularPhenotypeIntegrin alpha6Mutagenesis, Site-DirectedSequence Homology, Amino AcidRecombinant ProteinsProtein TransportHemidesmosomesTime FactorsSignal TransductionCloning, MolecularProteinuriaCell Adhesion MoleculesDNA Primers