Motor NeuronsMotor Neuron DiseaseNeuronsMusclesSurvival of Motor Neuron 1 ProteinNeurons, AfferentMuscle, SkeletalCell SurvivalMotor CortexSurvival of Motor Neuron 2 ProteinEvoked Potentials, MotorMuscle ProteinsSurvival RateMuscle, SmoothSpinal CordAmyotrophic Lateral SclerosisMuscle Fibers, SkeletalMuscle ContractionMuscle, Smooth, VascularMuscular Atrophy, SpinalMotor ActivityMuscle DevelopmentAxonsAction PotentialsSMN Complex ProteinsTime FactorsElectric StimulationCells, CulturedElectromyographyNerve Tissue ProteinsMuscle DenervationDisease-Free SurvivalImmunohistochemistryMuscle FatigueNeuromuscular DiseasesSurvivalMice, TransgenicNeuromuscular JunctionElectrophysiologyMolecular Motor ProteinsSynapsesMuscle Fibers, Fast-TwitchNerve DegenerationMovementGanglia, InvertebrateMuscle Fibers, Slow-TwitchDisease Models, AnimalMuscle SpindlesSynaptic TransmissionMice, Inbred C57BLSurvival AnalysisOculomotor MusclesNeck MusclesInterneuronsMitochondria, MuscleMyocytes, Smooth MuscleSignal TransductionSuperoxide DismutaseMembrane PotentialsAnimals, NewbornMutationGraft SurvivalRats, Sprague-DawleyMuscle, StriatedMuscle WeaknessCholinergic NeuronsAplysiaBrainPatch-Clamp TechniquesDopaminergic NeuronsSensory Receptor CellsMuscle RelaxationAnterior Horn CellsMuscular AtrophyCell DifferentiationMice, KnockoutRats, WistarNeural InhibitionDendritesGanglia, SpinalCalciumRNA, MessengerRespiratory MusclesBulbar Palsy, ProgressiveModels, NeurologicalCatsAnimals, Genetically ModifiedLocomotionGABAergic NeuronsAnalysis of VarianceFacial MusclesGene Expression Regulation, DevelopmentalFacial NerveNeural ConductionCerebral CortexPapillary MusclesCell CountHindlimbNeuropeptidesAbdominal Muscles