Muscular Atrophy, SpinalSpinal Muscular Atrophies of ChildhoodSurvival of Motor Neuron 1 ProteinSMN Complex ProteinsSurvival of Motor Neuron 2 ProteinMuscular AtrophyAtrophyCyclic AMP Response Element-Binding ProteinRNA-Binding ProteinsSpinal CordNerve Tissue ProteinsNeuronal Apoptosis-Inhibitory ProteinMuscular Disorders, AtrophicExonsMotor NeuronsAnterior Horn CellsMuscle, SkeletalBulbo-Spinal Atrophy, X-LinkedSpinal Cord InjuriesRibonucleoproteins, Small NuclearMusclesDEAD Box Protein 20Hindlimb SuspensionMuscle ProteinsChromosomes, Human, Pair 5Optic AtrophyMuscle Fibers, SkeletalDisease Models, AnimalMotor Neuron DiseaseSpinal Cord DiseasesSKP Cullin F-Box Protein LigasesCoiled BodiessnRNP Core ProteinsMuscle DenervationMuscle WeaknessMultiple System AtrophyMice, TransgenicPedigreeElectromyographyHeterozygote DetectionPhenotypeNeuromuscular DiseasesNeuromuscular JunctionGlycine-tRNA LigaseSpinal Nerve RootsInjections, SpinalGene DeletionMyostatinAxonsHomozygoteNerve DegenerationRNA SplicingNeuromuscular Junction DiseasesSpinal NervesArthrogryposisMuscle, SmoothMuscle ContractionMutationMagnetic Resonance ImagingContractureMuscle DevelopmentAnesthesia, SpinalNeural ConductionReceptors, AndrogenCharcot-Marie-Tooth DiseaseOlivopontocerebellar AtrophiesGene DosageVocal Cord ParalysisSpinal Cord NeoplasmsAmyotrophic Lateral SclerosisMuscle Fibers, Slow-TwitchSpinal CanalRNA, MessengerImmobilizationGenes, RecessiveMuscle Fibers, Fast-TwitchSpinal DiseasesMuscle, Smooth, VascularSpinal Cord CompressionGyrate AtrophyGenes, DominantFasciculationGenetic LinkageChemistry, AnalyticMice, KnockoutGene Expression RegulationSpinal NeoplasmsMolecular Sequence DataMuscular DiseasesPrenatal DiagnosisMotor ActivityAlternative SplicingSpliceosomesRespiratory ParalysisGenetic CounselingBulbar Palsy, ProgressiveMuscular DystrophiesTime FactorsCells, CulturedBase Sequence