Motor Neuron DiseaseMuscular Atrophy, SpinalMotor NeuronsMuscular AtrophyNeuromuscular DiseasesSpinal Muscular Atrophies of ChildhoodAtrophyBulbar Palsy, ProgressiveSurvival of Motor Neuron 1 ProteinSMN Complex ProteinsSpinal CordSurvival of Motor Neuron 2 ProteinAmyotrophic Lateral SclerosisMuscular Disorders, AtrophicMuscle, SkeletalNeuronsBulbo-Spinal Atrophy, X-LinkedAnterior Horn CellsMusclesMuscle ProteinsHindlimb SuspensionNerve DegenerationSKP Cullin F-Box Protein LigasesElectromyographyMuscle Fibers, SkeletalSpinal Cord InjuriesNerve Tissue ProteinsDisease Models, AnimalSuperoxide DismutaseAxonsSpinal Cord DiseasesFasciculationNeuronal Apoptosis-Inhibitory ProteinMice, TransgenicMuscle WeaknessCyclic AMP Response Element-Binding ProteinDEAD Box Protein 20Muscle DenervationRNA-Binding ProteinsNeural ConductionOptic AtrophyMotor CortexNeurons, AfferentNeurofilament ProteinsGaggingNeuromuscular JunctionInclusion BodiesMotor ActivityTDP-43 ProteinopathiesFrontotemporal Lobar DegenerationFrontotemporal DementiaMutationMuscle ContractionBrainEvoked Potentials, MotorSpinal Nerve RootsUlnar NerveRNA-Binding Protein FUSMuscle, SmoothToxascariasisbeta-Hexosaminidase beta ChainRiluzoleMyostatinPyrrolidonecarboxylic AcidPharyngostomyPeripheral NervesDeglutition DisordersElectric InjuriesPick Disease of the BrainMuscle DevelopmentMultiple System AtrophyAction PotentialsElectric StimulationParalysisTime FactorsPhenotypeCells, CulturedMice, Inbred C57BLPedigreeBrain Injury, ChronicMagnetic Resonance ImagingImmunohistochemistryLathyrismMuscle, Smooth, VascularNeurologic ExaminationMuscle Fibers, Slow-TwitchRibonucleoproteins, Small NuclearMuscle Fibers, Fast-TwitchMice, KnockoutDementiaImmobilizationReceptors, AndrogenRats, TransgenicAge of OnsetSandhoff DiseaseMarchiafava-Bignami DiseaseAxonal TransportRats, Sprague-DawleyCricoid CartilageRecruitment, Neurophysiological