Motor NeuronsSignal TransductionNeuronsMotor Neuron DiseaseSurvival of Motor Neuron 1 ProteinNeurons, AfferentMotor CortexSurvival of Motor Neuron 2 ProteinEvoked Potentials, MotorSpinal CordAmyotrophic Lateral SclerosisProtein Sorting SignalsMuscular Atrophy, SpinalMotor ActivityAxonsAction PotentialsSMN Complex ProteinsNerve Tissue ProteinsElectric StimulationSynapsesMolecular Motor ProteinsElectrophysiologySynaptic TransmissionThalamusInterneuronsCells, CulturedNerve DegenerationGanglia, InvertebrateNeuromuscular DiseasesMice, TransgenicMovementNeural InhibitionModels, NeurologicalDendritesPatch-Clamp TechniquesTime FactorsCerebral CortexBrainImmunohistochemistryElectromyographyMutationCholinergic NeuronsSensory Receptor CellsMolecular Sequence DataAplysiaDopaminergic NeuronsSuperoxide DismutaseNeuromuscular JunctionAnterior Horn CellsAnimals, NewbornMembrane PotentialsThalamic NucleiBrain StemGanglia, SpinalCatsgamma-Aminobutyric AcidBulbar Palsy, ProgressiveGABAergic NeuronsAfferent PathwaysAnimals, Genetically ModifiedDisease Models, AnimalExcitatory Postsynaptic PotentialsMice, Inbred C57BLAmino Acid SequenceHippocampusNerve NetReaction TimeEvoked PotentialsGreen Fluorescent ProteinsMedulla OblongataRats, Sprague-DawleyNeural ConductionAxonal TransportFacial NerveNeural PathwaysMotor Skills DisordersNeuronal PlasticityBehavior, AnimalNeuropeptidesCell DifferentiationCentral Nervous SystemLocomotionGlutamic AcidMice, KnockoutMuscle, SkeletalGrasshoppersPhysical StimulationCell CountCholine O-AcetyltransferaseGangliaNeurons, EfferentPsychomotor PerformanceGene Expression Regulation, DevelopmentalPeriodicityNeurofilament ProteinsModels, BiologicalGeniculate BodiesCalciumChick EmbryoRats, Wistar