Muscular Atrophy, SpinalSpinal Muscular Atrophies of ChildhoodMotor NeuronsSurvival of Motor Neuron 1 ProteinSMN Complex ProteinsSurvival of Motor Neuron 2 ProteinAtrophySpinal CordMuscular AtrophyMotor Neuron DiseaseNeuronsMuscular Disorders, AtrophicBulbo-Spinal Atrophy, X-LinkedSpinal Cord InjuriesAnterior Horn CellsNeuronal Apoptosis-Inhibitory ProteinCyclic AMP Response Element-Binding ProteinNerve Tissue ProteinsNeurons, AfferentMotor ActivityAmyotrophic Lateral SclerosisRNA-Binding ProteinsMotor CortexEvoked Potentials, MotorAxonsSpinal Cord DiseasesDisease Models, AnimalRibonucleoproteins, Small NuclearNerve DegenerationNeuromuscular DiseasesDEAD Box Protein 20Mice, TransgenicSpinal Nerve RootsElectromyographyAction PotentialsOptic AtrophyBulbar Palsy, ProgressiveMuscle, SkeletalSpinal NervesExonsNeuromuscular JunctionCoiled BodiesInjections, SpinalChromosomes, Human, Pair 5Ganglia, SpinalNeural ConductionMutationElectric StimulationSynapsesTime FactorsBrainCells, CulturedsnRNP Core ProteinsImmunohistochemistryPhenotypeMultiple System AtrophyInterneuronsReceptors, AndrogenMolecular Motor ProteinsAnesthesia, SpinalElectrophysiologyAnimals, NewbornSynaptic TransmissionMovementPhysical FitnessSuperoxide DismutaseGanglia, InvertebratePedigreeSpinal Cord NeoplasmsMusclesSpinal CanalSpinal Cord CompressionSpinal DiseasesNeurofilament ProteinsMuscle WeaknessRats, Sprague-DawleyCentral Nervous SystemMice, Inbred C57BLCholinergic NeuronsLocomotionCharcot-Marie-Tooth DiseaseMice, KnockoutAnimals, Genetically ModifiedSensory Receptor CellsSpinal NeoplasmsMolecular Sequence DataPeripheral NervesNeural InhibitionDendritesBrain StemCerebral CortexAplysiaAnalysis of VariancePatch-Clamp TechniquesMagnetic Resonance ImagingDopaminergic NeuronsArthrogryposisGene DeletionHeterozygote DetectionSciatic Nerve