Muscular Atrophy, SpinalMuscular DystrophiesMotor NeuronsSpinal Muscular Atrophies of ChildhoodMuscular Dystrophy, DuchenneSurvival of Motor Neuron 1 ProteinMuscular Dystrophy, AnimalSMN Complex ProteinsSurvival of Motor Neuron 2 ProteinAtrophySpinal CordMuscular AtrophyMotor Neuron DiseaseDystrophinMyotonic DystrophyMuscular Dystrophies, Limb-GirdleNeuronsMuscular Dystrophy, FacioscapulohumeralMice, Inbred mdxMuscular Dystrophy, Emery-DreifussSarcoglycansMuscular Disorders, AtrophicMuscle, SkeletalBulbo-Spinal Atrophy, X-LinkedSpinal Cord InjuriesCorneal Dystrophies, HereditaryAnterior Horn CellsNeuronal Apoptosis-Inhibitory ProteinDystroglycansCyclic AMP Response Element-Binding ProteinNerve Tissue ProteinsMuscular Dystrophy, OculopharyngealNeurons, AfferentUtrophinRNA-Binding ProteinsDisease Models, AnimalAmyotrophic Lateral SclerosisNeuromuscular DiseasesExonsMotor CortexPedigreeEvoked Potentials, MotorMotor ActivityMutationAxonsMusclesHeterozygote DetectionMice, TransgenicSpinal Cord DiseasesFuchs' Endothelial DystrophyPhenotypeElectromyographyMuscle Fibers, SkeletalThymopoietinsNerve DegenerationRibonucleoproteins, Small NuclearNeuromuscular JunctionDEAD Box Protein 20Retinal DystrophiesCollagen Type VIImmunohistochemistryAction PotentialsSpinal Nerve RootsOptic AtrophyBulbar Palsy, ProgressiveMuscle ProteinsCells, CulturedMuscle WeaknessChromosomes, Human, Pair 5Mice, Inbred C57BLSpinal NervesGenetic LinkageMolecular Sequence DataMuscular DiseasesBrainGenes, RecessiveSarcolemmaDystrophin-Associated ProteinsMice, KnockoutCoiled BodiesTime FactorsCreatine KinaseInjections, SpinalSynapsesGanglia, SpinalMyoblastsNeural ConductionElectric StimulationHomozygoteGene DeletionGenetic TherapyGenes, DominantX ChromosomeTrinucleotide Repeat ExpansionAnimals, NewbornLamininsnRNP Core ProteinsBase SequenceChromosomes, Human, Pair 4Lamin Type A