Motor Neuron DiseaseMotor NeuronsMuscular Atrophy, SpinalNeuromuscular DiseasesSpinal Muscular Atrophies of ChildhoodSurvival of Motor Neuron 1 ProteinBulbar Palsy, ProgressiveSpinal CordSurvival of Motor Neuron 2 ProteinSMN Complex ProteinsNeuronsAmyotrophic Lateral SclerosisMuscular AtrophyAtrophyAnterior Horn CellsMuscular Disorders, AtrophicBulbo-Spinal Atrophy, X-LinkedNeurons, AfferentMotor CortexNerve DegenerationAxonsNerve Tissue ProteinsEvoked Potentials, MotorMotor ActivitySuperoxide DismutaseElectromyographySpinal Cord InjuriesCyclic AMP Response Element-Binding ProteinFasciculationDisease Models, AnimalSpinal Cord DiseasesMice, TransgenicDEAD Box Protein 20Neuronal Apoptosis-Inhibitory ProteinRNA-Binding ProteinsNeurofilament ProteinsNeural ConductionAction PotentialsNeuromuscular JunctionMutationGaggingTDP-43 ProteinopathiesInclusion BodiesBrainMuscle, SkeletalFrontotemporal DementiaFrontotemporal Lobar DegenerationSpinal Nerve RootsRNA-Binding Protein FUSElectric StimulationPeripheral NervesUlnar NerveRiluzoleToxascariasisPyrrolidonecarboxylic Acidbeta-Hexosaminidase beta ChainCells, CulturedPharyngostomyImmunohistochemistryElectric InjuriesDeglutition DisordersSynapsesAxonal TransportPick Disease of the BrainParalysisMusclesTime FactorsMolecular Motor ProteinsAnimals, Genetically ModifiedBrain Injury, ChronicGanglia, SpinalPhenotypeRibonucleoproteins, Small NuclearMuscle WeaknessLathyrismPedigreeRats, TransgenicInterneuronsGanglia, InvertebrateElectrophysiologyNeurologic ExaminationMice, Inbred C57BLSynaptic TransmissionRecruitment, NeurophysiologicalMovementSandhoff DiseaseMarchiafava-Bignami DiseaseCholinergic NeuronsDementiaAge of OnsetReceptors, AndrogenSpinal NervesAnimals, NewbornMice, KnockoutCell CountDNA Repeat ExpansionAplysiaSensory Receptor CellsCricoid CartilageDopaminergic Neurons