Motor NeuronsMitochondriaMotor Neuron DiseaseNeuronsMusclesMitochondria, LiverSurvival of Motor Neuron 1 ProteinNeurons, AfferentMuscle, SkeletalMitochondria, MuscleMitochondria, HeartMotor CortexMuscle ProteinsEvoked Potentials, MotorSurvival of Motor Neuron 2 ProteinMuscle, SmoothSpinal CordAmyotrophic Lateral SclerosisMuscle Fibers, SkeletalMuscle ContractionMuscle, Smooth, VascularMotor ActivityMuscular Atrophy, SpinalMuscle DevelopmentAxonsAction PotentialsCells, CulturedElectric StimulationSMN Complex ProteinsElectromyographyMitochondrial ProteinsNerve Tissue ProteinsMuscle DenervationMembrane PotentialsTime FactorsCalciumMuscle FatigueNeuromuscular DiseasesElectrophysiologyNeuromuscular JunctionMuscle Fibers, Fast-TwitchMolecular Motor ProteinsSynapsesNerve DegenerationMice, TransgenicSuperoxide DismutaseMovementImmunohistochemistryRats, WistarRats, Sprague-DawleyMuscle Fibers, Slow-TwitchGanglia, InvertebrateOxidative PhosphorylationOxygen ConsumptionMutationMitochondrial SwellingSynaptic TransmissionMolecular Sequence DataMuscle SpindlesOculomotor MusclesBrainMyocytes, Smooth MuscleNeck MusclesMitochondrial MembranesDisease Models, AnimalInterneuronsIntracellular MembranesMicroscopy, ElectronMuscle, StriatedAdenosine TriphosphateMice, Inbred C57BLAnimals, NewbornPatch-Clamp TechniquesMuscle WeaknessSignal TransductionAplysiaCholinergic NeuronsMuscular AtrophyDopaminergic NeuronsSensory Receptor CellsModels, BiologicalApoptosisMuscle RelaxationDendritesAnterior Horn CellsRNA, MessengerCell RespirationKineticsAmino Acid SequenceGreen Fluorescent ProteinsGanglia, SpinalNeural InhibitionRespiratory MusclesMice, KnockoutModels, NeurologicalCatsBulbar Palsy, ProgressiveAnimals, Genetically ModifiedCerebral CortexAxonal Transport