SMN Complex ProteinsMotor NeuronsSurvival of Motor Neuron 1 ProteinMuscular Atrophy, SpinalSurvival of Motor Neuron 2 ProteinSpinal Muscular Atrophies of ChildhoodNeuronal Apoptosis-Inhibitory ProteinCyclic AMP Response Element-Binding ProteinMotor Neuron DiseaseNeuronsRNA-Binding ProteinsNerve Tissue ProteinsExonsNeurons, AfferentMotor CortexEvoked Potentials, MotorAmyotrophic Lateral SclerosisSpinal CordMotor ActivityAxonsAction PotentialsMolecular Motor ProteinsElectric StimulationNerve DegenerationSynapsesNeuromuscular DiseasesGanglia, InvertebrateElectrophysiologyInterneuronsSynaptic TransmissionMovementCholinergic NeuronsCells, CulturedAplysiaMice, TransgenicDopaminergic NeuronsSuperoxide DismutaseElectromyographyAnterior Horn CellsNeuromuscular JunctionDendritesSensory Receptor CellsBulbar Palsy, ProgressiveGanglia, SpinalNeural InhibitionGABAergic NeuronsPatch-Clamp TechniquesImmunohistochemistryModels, NeurologicalBrainCerebral CortexAnimals, NewbornDisease Models, AnimalTime FactorsFacial NerveMembrane PotentialsMotor Skills DisordersAnimals, Genetically ModifiedHippocampusgamma-Aminobutyric AcidBrain StemAxonal TransportNeuropeptidesMutationNeural ConductionCholine O-AcetyltransferaseGangliaGrasshoppersNeurons, EfferentNerve NetNeurofilament ProteinsLocomotionCentral Nervous SystemReaction TimeGreen Fluorescent ProteinsBehavior, AnimalMedulla OblongataExcitatory Postsynaptic PotentialsNeuronal PlasticityEvoked PotentialsCell CountMice, Inbred C57BLMuscle, SkeletalGene Expression Regulation, DevelopmentalOlfactory Receptor NeuronsGlutamic AcidPsychomotor PerformanceCatsAfferent PathwaysDopamineLeechesChick EmbryoRats, Sprague-DawleyMusclesNeurogliaRhombencephalonParalysisAnalysis of VariancePyramidal CellsRats, Wistar