Amino Acids, Branched-ChainAmino AcidsIsoleucineKeto AcidsValineLeucineMaple Syrup Urine DiseaseParenteral NutritionTransaminasesHepatic EncephalopathyAmmoniaNitrogenSarcoma, YoshidaSequence Homology, Amino AcidAmino Acid SequenceKineticsInsulinGlucoseLiverAmino Acid SubstitutionMolecular Sequence DataCloning, MolecularParenteral Nutrition, TotalProteinsPolymerase Chain ReactionAmino Acids, EssentialBase SequenceAmino Acid Transport SystemsSequence AlignmentMutationEscherichia coliBinding SitesAmino Acid MotifsProtein ConformationPeptide FragmentsDNA, ComplementaryModels, MolecularSequence Homology, Nucleic AcidRecombinant ProteinsMutagenesis, Site-DirectedAmino Acids, AromaticMolecular WeightProtein BindingProtein Structure, TertiaryDNAAmino Acids, SulfurPeptidesSubstrate SpecificityRNA, MessengerCell LineBacterial ProteinsElectrophoresis, Polyacrylamide GelStructure-Activity RelationshipRestriction MappingImmunoglobulin Light Chains