MitochondriaMitochondria, LiverProteasome Endopeptidase ComplexProteolysisMitochondria, HeartUbiquitinMitochondria, MuscleUbiquitin-Protein LigasesMitochondrial ProteinsUbiquitinationUbiquitinsCysteine EndopeptidasesMultienzyme ComplexesProteinsMolecular Sequence DataMuscle ProteinsMethylhistidinesAmino Acid SequenceEndoplasmic Reticulum-Associated DegradationAutophagyProteasome InhibitorsKineticsSaccharomyces cerevisiaePeptide HydrolasesEndoplasmic ReticulumMitochondrial SwellingIntracellular MembranesLeupeptinsCell LineMutationOxidative PhosphorylationProtein TransportMitochondrial MembranesAdenosine TriphosphateSKP Cullin F-Box Protein LigasesApoptosisCysteine Proteinase InhibitorsProtein Processing, Post-TranslationalCells, CulturedLysosomesLeucineModels, BiologicalMuscular AtrophyOxygen ConsumptionProtein BindingSignal TransductionAdenosine TriphosphatasesSaccharomyces cerevisiae ProteinsCytosolOxidation-ReductionCell RespirationCarrier ProteinsHydrolysisEndopeptidasesDNA, MitochondrialF-Box ProteinsAmino AcidsBiodegradation, EnvironmentalMembrane ProteinsCytochromes cMembrane Potential, MitochondrialProtein StabilityEndopeptidase ClpReactive Oxygen SpeciesProtease InhibitorsProtein BiosynthesisMitochondrial Membrane Transport ProteinsRNA, MessengerUncoupling AgentsBiological TransportElectron Transport Complex IVTime FactorsMicroscopy, ElectronHeLa CellsBase SequenceLiverBlotting, WesternMuscle, SkeletalATP-Dependent ProteasesProtein Structure, TertiaryUbiquitin-Conjugating EnzymesLigasesPolyubiquitinMolecular ChaperonesOligomycinsMalatesSubcellular FractionsCell Line, TumorCattleOxidative StressCalciumPhosphorylationUbiquitinated ProteinsCalpainCell NucleusCytochrome c GroupFungal ProteinsRotenoneCullin ProteinsSubstrate Specificity