DNA, MitochondrialMitochondriaMitochondrial DiseasesEnergy MetabolismLipid MetabolismGenome, MitochondrialPhylogenyHaplotypesBase SequenceGenes, MitochondrialMolecular Sequence DataMutationGenetic VariationElectron Transport Complex IVMitochondrial MyopathiesMitochondrial ProteinsNADH DehydrogenaseMELAS SyndromeKearns-Sayre SyndromeSequence Analysis, DNAMitochondrial EncephalomyopathiesCytochromes bGenetics, PopulationOphthalmoplegia, Chronic Progressive ExternalGlucoseDNA-Directed DNA PolymeraseMetabolismOptic Atrophy, Hereditary, LeberMERRF SyndromePolymerase Chain ReactionDNA ReplicationEthidiumOxidative PhosphorylationEvolution, MolecularLiverRNA, Transfer, LeuPhylogeographySpecies SpecificityDNA, KinetoplastCell NucleusGeographyElectron Transport Complex IPoint MutationMitochondria, MuscleSaccharomyces cerevisiaeDNA, FungalOxygen ConsumptionOxidation-ReductionLeigh DiseaseDNA DamageDNA PrimersPolymorphism, Restriction Fragment LengthOxidative StressPhenotypeKineticsBiological EvolutionGlycolysisPolymorphism, GeneticChromosomes, Human, YForensic AnthropologyGene DosageGene DeletionModels, GeneticOptic Atrophies, HereditaryMuscle, SkeletalReactive Oxygen SpeciesDNAMitochondrial Proton-Translocating ATPasesBiotransformationCell RespirationRNA, RibosomalAgingHistory, AncientRNA, TransferAmino Acid SequenceGene FlowMitochondria, LiverDNA Mutational AnalysisModels, BiologicalExtrachromosomal InheritanceSequence DeletionSiberiaDiffuse Cerebral Sclerosis of SchilderRNATime FactorsMicrosomes, LiverCytochrome P-450 Enzyme SystemDNA, CircularNucleic Acid ConformationCell LineLactic AcidTranscription, GeneticCytochrome b GroupCrithidia fasciculataAdenosine TriphosphateRNA, MessengerChromatography, High Pressure LiquidDNA Restriction EnzymesMetabolic Networks and PathwaysCells, Cultured