Hepatolenticular DegenerationMetallochaperonesCation Transport ProteinsCopperMenkes Kinky Hair SyndromeAdenosine TriphosphatasesRats, Inbred LECCeruloplasminHeavy Chain DiseaseTrientineCarrier ProteinsMachado-Joseph DiseasePenicillamineExtrapyramidal TractsMutationHeredodegenerative Disorders, Nervous SystemChelating AgentsChromosomes, Human, Pair 13Chelation TherapyRats, Mutant StrainsMolecular Sequence DataRecombinant Fusion ProteinsNerve Tissue ProteinsImmunoglobulin gamma-ChainsAmino Acid SequenceGolgi ApparatusMolecular ChaperonesBrain Diseases, MetabolicNeurodegenerative DiseasesCarboxylesteraseBase SequenceProtein TransportDNA PrimersCell LineDNA Mutational AnalysisProtein Structure, TertiaryMetal Metabolism, Inborn ErrorsPeptidesModels, MolecularProteostasis DeficienciesNuclear ProteinsDisease Models, AnimalLiverHuntington DiseaseProtein BindingSpinocerebellar AtaxiasSaccharomyces cerevisiaeBiological TransportPhenotypeLiver Function TestsMutation, MissenseInclusion BodiesDimethyldithiocarbamateZincHepatocytesProtein ConformationDNA, ComplementaryRepressor ProteinsUbiquitinTRPP Cation ChannelsTrinucleotide Repeat ExpansionPedigreeBinding SitesGenetic MarkersIronSequence Homology, Amino Acid