Maple Syrup Urine DiseaseAcerKetone OxidoreductasesNutritive SweetenersAmino Acids, Branched-ChainKeto AcidsNorleucineMultienzyme ComplexesPlant PoisoningMethemoglobinemiaPhyllachoralesIsoleucineLeucineQuercusTreesPhenylketonuriasThiaminePlant LeavesLignansRats, Inbred OLETFNutritional RequirementsMutationDietary Proteins