CystineLysosomesCystinosisCystine Knot MotifsAmino Acid Transport System y+CysteamineCystinuriaLysosome-Associated Membrane GlycoproteinsCysteineEndosomesFanconi SyndromeAmino Acids, SulfurCyclotidesAcid PhosphataseEndocytosisPhagosomesGlutathioneDisulfidesAmino AcidsCathepsin DCystamineAmino Acid Transport Systems, NeutralBiological TransportMethionineAutophagyAmino Acid Transport Systems, BasicOldenlandiaLysosomal-Associated Membrane Protein 2Microscopy, ElectronCystine-Knot MiniproteinsSulfhydryl CompoundsHydrogen-Ion ConcentrationCathepsinsCells, CulturedCoprophagiaProtein TransportVacuolesMucolipidosesLiverFibroblastsCell LineAmino Acid SequenceChediak-Higashi SyndromeChloroquineKineticsMaleatesbeta-N-AcetylhexosaminidasesMolecular Sequence DataReceptor, IGF Type 2Cell FractionationGolgi ApparatusCell Membranerab GTP-Binding ProteinsSubcellular FractionsMannosephosphatesOrganellesIntracellular MembranesGlucuronidaseOxidation-Reduction