Muscular Atrophy, SpinalMotor Neuron DiseaseMotor NeuronsSpinal Muscular Atrophies of ChildhoodSurvival of Motor Neuron 1 ProteinSMN Complex ProteinsSpinal CordAmyotrophic Lateral SclerosisNeuromuscular DiseasesMuscular AtrophySurvival of Motor Neuron 2 ProteinAtrophyToxascariasisAnterior Horn CellsNeuronsBulbar Palsy, ProgressiveFacial ParalysisElectromyographyMusclesMuscle, SkeletalNerve DegenerationMuscle WeaknessNeural ConductionMuscular Disorders, AtrophicUrinary Bladder, NeurogenicDisease Models, AnimalBulbo-Spinal Atrophy, X-LinkedSpinal Cord InjuriesParalysisNeuronal Apoptosis-Inhibitory ProteinCyclic AMP Response Element-Binding ProteinNerve Tissue ProteinsNeurons, AfferentPedigreeMice, TransgenicSyndromeSuperoxide DismutaseRNA-Binding ProteinsMotor CortexMutationMuscle ProteinsEvoked Potentials, MotorMuscle Fibers, SkeletalMuscle, SmoothMotor ActivityAxonsMuscle ContractionSpinal Cord DiseasesMuscle, Smooth, VascularRibonucleoproteins, Small NuclearAction PotentialsMuscle DevelopmentMuscle DenervationNeuromuscular JunctionDEAD Box Protein 20Spinal Nerve RootsElectric StimulationBrainOptic AtrophyCells, CulturedSpinal NervesExonsTime FactorsImmunohistochemistryCoiled BodiesInjections, SpinalGanglia, SpinalSynapsesChromosomes, Human, Pair 5Magnetic Resonance ImagingMuscle FatigueElectrophysiologyPhenotypeRats, Sprague-DawleyMovementMuscle Fibers, Fast-TwitchsnRNP Core ProteinsAnimals, NewbornSynaptic TransmissionMice, Inbred C57BLInterneuronsMultiple System AtrophyReceptors, AndrogenMuscle Fibers, Slow-TwitchMolecular Motor ProteinsAnesthesia, SpinalMice, KnockoutRNA, MessengerLocomotionGanglia, InvertebrateMuscle SpindlesMolecular Sequence DataSpinal Cord NeoplasmsNeck MusclesOculomotor MusclesMitochondria, MuscleCatsSpinal CanalNeurofilament ProteinsMembrane Potentials