Motor Neuron DiseaseToxascariasisMotor NeuronsNeuromuscular DiseasesAmyotrophic Lateral SclerosisBulbar Palsy, ProgressiveMuscular Atrophy, SpinalReflexSurvival of Motor Neuron 1 ProteinSpinal CordAnterior Horn CellsSMN Complex ProteinsNeuronsNerve DegenerationElectromyographyFacial ParalysisMuscular AtrophyNeural ConductionSuperoxide DismutaseSpinal Muscular Atrophies of ChildhoodMuscle WeaknessParalysisSurvival of Motor Neuron 2 ProteinUrinary Bladder, NeurogenicDisease Models, AnimalGaggingNeurons, AfferentMuscle, SkeletalMice, TransgenicMutationMotor CortexMuscular Disorders, AtrophicSyndromePedigreeFasciculationBulbo-Spinal Atrophy, X-LinkedAxonsReflex, StretchTDP-43 ProteinopathiesReflex, AbnormalFrontotemporal Lobar DegenerationNeurofilament ProteinsFrontotemporal DementiaEvoked Potentials, Motorbeta-Hexosaminidase beta ChainRNA-Binding Protein FUS