DeafnessAge of OnsetHearing Loss, SensorineuralPedigreeGenes, RecessiveCochleaHearing LossMutationSyndromeCerebellar AtaxiaPhenotypeEar, InnerEvoked Potentials, Auditory, Brain StemConnexinsAlzheimer DiseaseHearing Loss, UnilateralHair Cells, AuditoryTime FactorsDNA Mutational AnalysisGenetic LinkageSpiral GanglionStria VascularisHearingAllelesGenotypeGenes, DominantHeterozygoteOrnithine Carbamoyltransferase Deficiency DiseaseCochlear ImplantsAudiometryHearing Loss, BilateralHomozygoteAge FactorsInfant, NewbornMutation, MissenseConsanguinityAtaxiaOsteochondrosisCochlear ImplantationGenetic TestingGenetic Predisposition to DiseaseUsher SyndromesChromosome MappingHeterozygote DetectionSural NerveMyelin P0 ProteinBrainLipreadingHearing TestsHearing Loss, CentralMagnetic Resonance ImagingEndolymphMolecular Sequence DataRetrospective StudiesLod ScoreCharcot-Marie-Tooth DiseasePoint MutationWolfram SyndromeFamily HealthAuditory ThresholdCochlear NerveExonsRisk FactorsCerebrospinal Fluid OtorrheaHuntington DiseaseSpinocerebellar DegenerationsApolipoproteins EOrgan of CortiSign LanguageWaardenburg SyndromeHypoparathyroidismAudiometry, Pure-ToneHair Cells, Auditory, InnerHaplotypesDNA, MitochondrialGene FrequencyIntensive Care Units, NeonatalJervell-Lange Nielsen SyndromeBase SequenceStereociliaSeverity of Illness IndexCochlear DiseasesDisease Models, AnimalTectorial MembraneVestibular DiseasesLeukodystrophy, MetachromaticStapesCase-Control StudiesGlucose Metabolism DisordersNational Institute on Aging (U.S.)Friedreich AtaxiaTranscription Factor Brn-3CHearing DisordersPolymorphism, GeneticAtrophySepsisPolymerase Chain ReactionApolipoprotein E4Follow-Up StudiesInfant, Premature, Diseases