Acidosis, LacticAcidosisLactatesMELAS SyndromeLactic AcidAcidosis, RespiratoryPhenforminAcidosis, Renal TubularRNA, Transfer, LeuDichloroacetic AcidMitochondrial EncephalomyopathiesPyruvate Dehydrogenase Complex Deficiency DiseaseMetforminDiabetic KetoacidosisAcid-Base EquilibriumMitochondrial MyopathiesSodium BicarbonateMERRF SyndromeHydrogen-Ion ConcentrationDNA, MitochondrialAlkalosisBicarbonatesMitochondrial DiseasesL-Lactate DehydrogenaseLeigh DiseaseStavudineThiamine DeficiencyPyruvate Dehydrogenase (Lipoamide)Hyperglycemic Hyperosmolar Nonketotic ComaThyroid CrisisBiguanidesCarbon DioxideOxygen ConsumptionPyruvatesFatal OutcomeHypoglycemic AgentsMitochondria, MuscleBarth SyndromeCytochrome-c Oxidase Deficiency