Acidosis, LacticAcidosisMELAS SyndromeOxygenAcidosis, RespiratoryPhenforminAcidosis, Renal TubularRNA, Transfer, LeuLactatesMitochondrial EncephalomyopathiesLactic AcidDichloroacetic AcidPyruvate Dehydrogenase Complex Deficiency DiseaseOxygen ConsumptionMetforminDiabetic KetoacidosisMitochondrial MyopathiesSodium BicarbonateAcid-Base EquilibriumMERRF SyndromeReactive Oxygen SpeciesDNA, MitochondrialAlkalosisMitochondrial DiseasesHydrogen-Ion ConcentrationBicarbonatesLeigh DiseaseStavudineThiamine DeficiencyHyperglycemic Hyperosmolar Nonketotic ComaThyroid CrisisBiguanidesCarbon DioxidePyruvate Dehydrogenase (Lipoamide)MitochondriaFatal OutcomeMitochondria, MuscleBarth SyndromeOxygen Inhalation TherapyCytochrome-c Oxidase DeficiencyHypoglycemic Agents