• Heterotaxy, also referred to as isomerism of the atrial appendages, is defined as an abnormal assembly of the thoracic and abdominal organs from the normal arrangement known as 'situs solitus. (uptodate.com)
  • See 'Anatomy, clinical manifestations, and diagnosis of heterotaxy (isomerism of the atrial appendages)' . (uptodate.com)
  • The term 'isomerism,' derived from Greek ( iso, meaning 'equal,' and meros , meaning 'part'), refers to this abnormal developmental symmetry in which morphologic structures that normally develop on one side or the other of the body are found on both sides of the body, and is the currently accepted term used to describe hearts with isomeric atria and atrial appendages [ 1 ]. (uptodate.com)
  • So, in affected patients, instead of a distinct left and right side, individuals with isomerism will have either two right sides or two left sides resulting in either two right atria or two left atria (atrial isomerism) [ 2 ]. (uptodate.com)
  • Atrial isomerism is a major component of heterotaxy and causes significant morbidity and mortality because of discordance among the heart, systemic and pulmonary vessels, and other organs, and also among components of the heart. (uptodate.com)
  • Right atrial appendage isomerism - Right atrial appendage isomerism, also referred to as right atrial isomerism (RAI), results in two right sides with bilateral right atria and atrial appendages, and an absence of left-sided structures (eg, coronary sinus). (uptodate.com)
  • See 'Anatomy, clinical manifestations, and diagnosis of heterotaxy (isomerism of the atrial appendages)', section on 'Right atrial isomerism' . (uptodate.com)
  • The Outcome of Patients With Right Atrial Isomerism is Poor. (biomedsearch.com)
  • Right-atrial isomerism (RAI) is a heterotaxy syndrome with disturbances of left-right axis development resulting in complex heart malformations and anomalies of the thoracic and abdominal organs. (biomedsearch.com)
  • Intestinal obstruction caused by malrotation of the gut in atrial isomerism. (bmj.com)
  • Isomerism , the existence of molecules that have the same numbers of the same kinds of atoms (and hence the same formula) but differ in chemical and physical properties. (britannica.com)
  • The isomerism impact on the optical, electrochemical and photophysical properties and the photovoltaic performance is systematically investigated. (rsc.org)
  • This topic will review the management and outcome of patients with heterotaxy (isomerism). (uptodate.com)
  • The anatomical variation, clinical manifestations, and diagnosis of heterotaxy (isomerism) are presented separately. (uptodate.com)
  • It is not to be confused with E - Z isomerism , which is an absolute stereochemical description, and only to be used with alkenes. (wikipedia.org)
  • In lung and heart in which Pitx2 is expressed asymmetrically, right pulmonary isomerism, atrioventricular canals with prominent swelling, and juxtaposition of the atrium were detected. (biologists.org)
  • You can easily have a mixture of chain isomerism and position isomerism - you aren't restricted to one or the other. (studyvilla.com)
  • In position isomerism, the basic carbon skeleton remains unchanged, but important groups are moved around on that skeleton. (studyvilla.com)
  • The molecular formula, and the structural formula are the same, but the displayed formula is different - E/Z isomerism. (getrevising.co.uk)
  • The isomerism results in a dramatic change in shape as the rhodopsin is converted to meta-rhodopsin. (thecatalyst.org)