Cystic FibrosisInflammationCystic Fibrosis Transmembrane Conductance RegulatorFibrosisPseudomonas InfectionsPseudomonas aeruginosaInflammation MediatorsSputumLungSweatMice, Inbred CFTRBurkholderia InfectionsBurkholderia cepaciaDisease Models, AnimalChloridesEndomyocardial FibrosisIdiopathic Pulmonary FibrosisMice, Inbred C57BLRespiratory MucosaLiver CirrhosisExocrine Pancreatic InsufficiencyChloride ChannelsRespiratory SystemNasal MucosaForced Expiratory VolumeEpithelial CellsMice, KnockoutTobramycinRespiratory Function TestsBronchoalveolar Lavage FluidLung DiseasesRetroperitoneal FibrosisPancreatinNeonatal ScreeningBronchiCytokinesPneumoniaMucusBronchiectasisBurkholderia cepacia complexCells, CulturedBiological MarkersMutationPancreatic ExtractsNeutrophilsAnti-Inflammatory AgentsChronic DiseaseAnti-Bacterial AgentsLung TransplantationRNA, MessengerCell LineBleomycinTime FactorsTracheaExpectorantsHeterozygote DetectionTumor Necrosis Factor-alphaMeconiumInterleukin-8Signal TransductionAlginatesInterleukin-6MacrophagesLeukocyte ElastaseAdministration, InhalationPhenotypePancrelipaseGene Expression RegulationAchromobacter denitrificansLipopolysaccharidesMucociliary ClearanceBurkholderia cenocepaciaVital CapacityImmunohistochemistryEpitheliumAspergillosis, Allergic BronchopulmonarySweat GlandsLiverC-Reactive ProteinNeurogenic InflammationGenotypeGene ExpressionSeverity of Illness IndexMice, Inbred BALB CBiopsyIon TransportRespiratory Tract InfectionsDisease ProgressionAminophenolsReverse Transcriptase Polymerase Chain ReactionOral Submucous FibrosisMolecular Sequence DataLiver Cirrhosis, ExperimentalMembrane ProteinsAsthmaMice, TransgenicTransforming Growth Factor betaPolymerase Chain ReactionRats, Sprague-DawleyFibroblasts