Neurodegenerative DiseasesMotor NeuronsNeuronsMotor Neuron DiseaseAmyotrophic Lateral SclerosisSurvival of Motor Neuron 1 ProteinNerve DegenerationNeurons, AfferentNerve Tissue ProteinsSurvival of Motor Neuron 2 ProteinSpinal CordBrainMotor CortexMuscular Atrophy, SpinalEvoked Potentials, MotorDisease Models, AnimalParkinson DiseaseHuntington DiseaseMotor ActivityMice, TransgenicAlzheimer Diseasetau ProteinsAxonsalpha-SynucleinNeuroprotective AgentsMutationSMN Complex ProteinsCells, CulturedInclusion BodiesCell DeathSuperoxide DismutaseTauopathiesMicrogliaAction PotentialsImmunohistochemistrySynapsesDopaminergic NeuronsMice, Inbred C57BLHeredodegenerative Disorders, Nervous SystemAxonal TransportCerebral CortexHippocampusProteostasis DeficienciesCentral Nervous SystemAstrocytesSignal TransductionCell SurvivalAnimals, Genetically ModifiedPrionsTime FactorsFrontotemporal Lobar DegenerationAmyloid beta-PeptidesModels, BiologicalOxidative StressSynucleinsPrion DiseasesSynaptic TransmissionFrontotemporal DementiaSpinocerebellar AtaxiasMitochondriaMolecular Motor ProteinsNeurogliaNeurofilament ProteinsElectric StimulationNeurotoxinsNeuromuscular DiseasesApoptosisElectrophysiologyGanglia, InvertebrateTrinucleotide Repeat ExpansionAnimals, NewbornAgingDendritesNeuromuscular JunctionParkinsonian DisordersDopamineGreen Fluorescent ProteinsCerebellumGuamMice, KnockoutCholinergic NeuronsInterneuronsRNA-Binding Protein FUSBehavior, AnimalModels, NeurologicalGlutamic AcidPhenotypeNeurogenesisGene Expression RegulationRats, Sprague-DawleyMolecular Sequence DataAutophagySubstantia NigraFriedreich AtaxiaMovementGanglia, SpinalSensory Receptor CellsCell DifferentiationAnterior Horn CellsPatch-Clamp Techniques