Motor NeuronsSMN Complex ProteinsSurvival of Motor Neuron 1 ProteinMuscular Atrophy, SpinalSurvival of Motor Neuron 2 ProteinAmyotrophic Lateral SclerosisCell SurvivalSpinal Muscular Atrophies of ChildhoodNeuronsCyclic AMP Response Element-Binding ProteinSpinal CordMotor Neuron DiseaseRNA-Binding ProteinsNerve Tissue ProteinsSuperoxide DismutaseNeuronal Apoptosis-Inhibitory ProteinNeurons, AfferentCoiled BodiesMotor CortexRibonucleoproteins, Small NuclearSurvival RateExonsEvoked Potentials, MotorGemini of Coiled BodiesAxonsIndoprofenDisease Models, AnimalCells, CulturedMice, TransgenicMotor ActivityMutationDEAD Box Protein 20Neuropil ThreadsNeuromuscular JunctionNeuromuscular Junction DiseasesImmunohistochemistryNerve DegenerationAction PotentialsTime FactorsMolecular Sequence DataDisease-Free SurvivalMice, KnockoutNerve Growth FactorsRNA SplicingSurvivalsnRNP Core ProteinsAlternative SplicingAnimals, NewbornMolecular Motor ProteinsGene DeletionGanglia, SpinalElectric StimulationSynapsesChromosomes, Human, Pair 5Neuromuscular DiseasesBrain-Derived Neurotrophic FactorPhenotypeGanglia, InvertebrateGene DosageRNA, MessengerSurvival AnalysisNeuritesMice, Inbred C57BLElectrophysiologyCell DeathMuscle, SkeletalCell LineInterneuronsSignal TransductionHippocampusSynaptic TransmissionSpliceosomesBrainBase SequenceAmino Acid SequenceGraft SurvivalFibroblastsMesencephalonCell CountMovementCholinergic NeuronsRats, Sprague-DawleyAplysiaHomozygoteDopaminergic NeuronsHeterozygote DetectionNeurogenesisNeurotrophin 3HeLa CellsCentral Nervous SystemSpiral GanglionElectromyographyAnterior Horn CellsApoptosisDendritesSensory Receptor CellsBlotting, WesternGene Expression Regulation, DevelopmentalBulbar Palsy, ProgressivePatch-Clamp Techniques