GangliosidosesLipidosesHexosaminidase AHexosaminidase BHexosaminidasesG(M2) GangliosideG(M1) Gangliosidebeta-N-AcetylhexosaminidasesG(M3) GangliosideTay-Sachs DiseaseGangliosidesSandhoff DiseaseG(M2) Activator ProteinSphingolipid Activator ProteinsAcetylglucosaminidaseInterleukin-1betaGangliosidoses, GM2Chromosomes, Human, 4-5Molecular Sequence DataHymecromonebeta 2-MicroglobulinChromatography, Thin LayerSaposinsIsoenzymesAmino Acid SequenceElectrophoresis, Starch GelCell LineKineticsReceptors, Adrenergic, betaIntegrin beta3GlycosphingolipidsSialyltransferasesLysosomesCarbohydrate SequenceMacromolecular SubstancesAcetylglucosamineChromosomes, Human, 13-15Base SequencePolymerase Chain ReactionCells, CulturedReceptors, Antigen, T-Cell, alpha-betaNeuraminidaseCholera ToxinSialic AcidsHeterozygote DetectionIsoelectric FocusingTransforming Growth Factor betaMolecular WeightHexosaminesFibroblastsProtein ConformationElectrophoresis, Polyacrylamide GelRNA, MessengerAntibodies, MonoclonalMutationIntegrin alpha5beta1Chromatography, Ion ExchangeLiverSubstrate SpecificityHemoglobins, AbnormalGlycolipidsBinding SitesHydrogen-Ion ConcentrationCarbohydrate ConformationIntegrin beta4Integrin beta ChainsHot Temperature