Congenital HyperinsulinismHyperinsulinismSulfonylurea ReceptorsReceptors, DrugPotassium Channels, Inwardly RectifyingDiazoxideHypoglycemiaDiagnostic Techniques, EndocrineHyperammonemiaGlutamate DehydrogenaseATP-Binding Cassette TransportersPancreatectomyInsulinInsulinomaKATP ChannelsInsulin AntibodiesSulfonylurea CompoundsBeckwith-Wiedemann Syndrome3-Hydroxyacyl CoA DehydrogenasesPotassium ChannelsFocal AdhesionsInfant, NewbornCongenital Disorders of GlycosylationCyclin-Dependent Kinase Inhibitor p57MutationChromosomes, Human, Pair 11Islets of LangerhansTolbutamideInsulin-Secreting CellsHyperandrogenismBlood GlucoseMutation, MissenseChlorthalidoneOctreotidePancreasProinsulinHamartomaC-PeptideHeterozygoteSeizuresPancreatic NeoplasmsMosaicismHypopituitarismPedigreeGenes, DominantAmmoniaSyndromeAdenosine TriphosphateGlucoseHomozygoteGlucose Tolerance TestPoint MutationHyperplasiaGlomerulosclerosis, Focal Segmental