Loading...
  • dysplasia
  • McCune-Albright syndrome occurs when fibrous dysplasia is accompanied by the appearance of scattered areas of melanotic skin pigmentation (cafe-au-lait spots) and sexual precocity. (thefreedictionary.com)
  • Fibrous dysplasia of the jaws: Integrating molecular pathogenesis with clinical, radiological, and histopathological features. (nih.gov)
  • Fibrous dysplasia of skull base. (unicamp.br)
  • Bednar Tumor
  • 54 Bednar tumor is a rare variant of dermatofibrosarcoma protuberans (DFSP), a soft tissuesarcoma that develops in the deep layers of the skin. (malacards.org)
  • Bednar tumor is also known as pigmented DFSP because it contains dark-colored cells that give may give the tumor a multi-colored (i.e red and brown) appearance. (malacards.org)
  • The underlying cause of Bednar tumor is unknown. (malacards.org)
  • Bednar Tumor, also known as pigmented dermatofibrosarcoma protuberans , is related to dermatofibrosarcoma protuberans and ring chromosome 4 . (malacards.org)
  • An important gene associated with Bednar Tumor is PDGFB (Platelet Derived Growth Factor Subunit B), and among its related pathways/superpathways are Embryonic and Induced Pluripotent Stem Cell Differentiation Pathways and Lineage-specific Markers and Neural Stem Cell Differentiation Pathways and Lineage-specific Markers . (malacards.org)
  • vascular
  • Coffin CM, Dehner LP (1993) Vascular tumors in children and adolescents: a clinicopathologic study of 228 tumors in 222 patients. (springer.com)
  • Other less common primary spinal tumors include sarcomas, astrocytomas, vascular tumors, and chordomas, in decreasing order of frequency. (uchile.cl)
  • variant of dermatofibrosarcoma protuberans
  • Bednar tumour is a rare pigmented variant of dermatofibrosarcoma protuberans of intermediate malignant potential. (hindawi.com)
  • The clinical history of a Bednar tumour developing close to the scar of a previous melanoma gives the opportunity of a critical and intriguing discussion about the potential origin of pigmented cells in this rare variant of dermatofibrosarcoma protuberans. (hindawi.com)
  • Alveolar
  • Prematurely erupted teeth with a firm, non-ulcerated, reddish-bluish tumor approximately 4 cm × 4 cm in size, extending from the alveolar ridge to the hard palate and covered by intact mucosa. (biomedcentral.com)
  • intracranial
  • Central nervous system changes occur as the lesions invade and destroy tissue, and, because the tumors compress the brain, cranial nerves, and cerebral blood vessels, the compression causes cerebral edema and increased intracranial pressure (ICP). (thefreedictionary.com)
  • neoplasms
  • Tumors are also called neoplasms , which means that they are composed of new and actively growing tissue. (thefreedictionary.com)
  • The familial tumor syndromes (and respective chromosomal abnormalities that are associated with CNS neoplasms) include neurofibromatosis type I (17q11), neurofibromatosis type II (22q12), von Hippel-Lindau disease (3p25-26), tuberous sclerosis (9q34, 16p13), Li-Fraumeni syndrome (17p13), Turcot syndrome type 1 (3p21, 7p22), Turcot syndrome type 2 (5q21), and nevoid basal cell carcinoma syndrome (9q22.3). (uchile.cl)
  • Neurofibroma
  • A neurilemmoma is a benign, usually encapsulated neoplasm derived from Schwann cells and, along with neurofibroma, constitutes one of the 2 most common benign peripheral nerve sheath tumors. (medscape.com)