Acidosis, LacticAcidosisMELAS SyndromeAcidosis, RespiratoryPhenforminAcidosis, Renal TubularRNA, Transfer, LeuLactatesMitochondrial EncephalomyopathiesDichloroacetic AcidLactic AcidPyruvate Dehydrogenase Complex Deficiency DiseaseMetforminDiabetic KetoacidosisMitochondrial MyopathiesSodium BicarbonateAcid-Base EquilibriumMERRF SyndromeDNA, MitochondrialAlkalosisMitochondrial DiseasesBicarbonatesHydrogen-Ion ConcentrationLeigh DiseaseStavudineThiamine DeficiencyHyperglycemic Hyperosmolar Nonketotic ComaThyroid CrisisBiguanidesPyruvate Dehydrogenase (Lipoamide)Fatal OutcomeBarth SyndromeCytochrome-c Oxidase DeficiencyHypoglycemic AgentsMitochondria, MuscleCarbon Dioxide