• Epithelioid Hemangioendothelioma is a rare form of cancer that affects the blood vessels of an individual and has an unknown etiology. (ipl.org)
  • Epithelioid Hemangioendothelioma affects about 0.1 percent of the American population with an overall 5-year survival rate of 55% after a standard primary radical treatment. (ipl.org)
  • Crazy sexy cancer is a documentary about a young lady, age 31, who was diagnosed with epithelioid Hemangioendothelioma, stage IV cancer on Valentine's day in 2003. (ipl.org)
  • Hepatic epithelioid hemangioendothelioma (HEHE) is a rare liver tumor, which is usually diagnosed by pathological examination, since the diagnostic imaging criteria remain to be defined. (spandidos-publications.com)
  • Hemangioendothelioma, Epithelioid" is a descriptor in the National Library of Medicine's controlled vocabulary thesaurus, MeSH (Medical Subject Headings) . (uchicago.edu)
  • It is unclear whether the epithelioid hemangioendothelioma is truly neoplastic or an exuberant tissue reaction, nor is it clear if this is equivalent to Kimura's disease (see ANGIOLYMPHOID HYPERPLASIA WITH EOSINOPHILIA). (uchicago.edu)
  • This graph shows the total number of publications written about "Hemangioendothelioma, Epithelioid" by people in this website by year, and whether "Hemangioendothelioma, Epithelioid" was a major or minor topic of these publications. (uchicago.edu)
  • Below are the most recent publications written about "Hemangioendothelioma, Epithelioid" by people in Profiles. (uchicago.edu)
  • Epithelioid Hemangioendothelioma: Update on Diagnosis and Treatment. (uchicago.edu)
  • Novel YAP1-TFE3 fusion defines a distinct subset of epithelioid hemangioendothelioma. (uchicago.edu)
  • Clinical patterns and outcome in epithelioid hemangioendothelioma with or without pulmonary involvement: insights from an internet registry in the study of a rare cancer. (uchicago.edu)
  • Mediastinal epithelioid hemangioendothelioma metastatic to lymph nodes and pleural fluid: report of a case. (uchicago.edu)
  • Epithelioid hemangioendothelioma of soft tissue: a proposal for risk stratification based on 49 cases. (uchicago.edu)
  • Left atrial epithelioid hemangioendothelioma. (uchicago.edu)
  • Foods for Epithelioid Hemangioendothelioma! (addon.life)
  • Introduction Foods for Epithelioid Hemangioendothelioma should be personalized for each individual and also must adapt when cancer treatment or tumor genetic change. (addon.life)
  • Epithelioid sarcoma (ES) is a rare, malignant soft tissue tumor. (logicalimages.com)
  • Malignant perivascular epithelioid cell tumor is a rare, aggressive sarcoma," wrote Andrew J. Wagner, MD, PhD, Medical Director of Ambulatory Oncology at Dana-Farber Cancer Institute and Associate Professor of Medicine at Harvard Medical School, and colleagues, in their publication of the AMPECT trial (NCT02494570), on which the approval was based. (oncdata.com)
  • In this paper we present a case of reconstruction of Achilles tendon defect with peroneus brevis transfer reinforced with medial gastrocnemius fascia and plantaris tendon after excision of a local recurrence of epithelioid sarcoma. (springeropen.com)
  • Epithelioid sarcoma arising from the Achilles tendon is an extremely rare malignant tumour in an atypical site and may easily be confused with other soft tissue masses. (springeropen.com)
  • In this paper we present a technical case of reconstruction of Achilles tendon defect with peroneus brevis transfer reinforced with medial gastrocnemius fascia and plantaris tendon after excision of a rare case of local recurrence of epithelioid sarcoma as an effective reconstructive strategy to obtain satisfactory functional results even after a wide resection as required. (springeropen.com)
  • Tazemetostat is used to treat epithelioid sarcoma (a rare, slow-growing soft tissue cancer) in adults and children 16 years of age and older that has spread to nearby tissues or to other parts of the body and cannot be treated successfully with surgery. (medlineplus.gov)
  • Long-term follow-up for duration of response (DoR) after weekly nab-sirolimus in patients with advanced malignant perivascular epithelioid cell tumors (PEComa): results from a registrational open-label phase II trial, AMPECT. (oncdata.com)
  • Perivascular epithelioid cell tumour (PEComa) is a rare family of mesenchymal tumours composed of epithelioid cells. (jpccr.eu)
  • Handa A, Fujita K, Kono T, Komori K, Hirobe S, Fukuzawa R. Radiological findings of perivascular epithelioid cell tumour (PEComa) of the falciform ligament. (jpccr.eu)
  • Perivascular epithelioid cell tumor (PEComa) occurring in the female genital tract are rare, and typically found in the uterine corpus. (biomedcentral.com)
  • The cytologic characteristics of the tumor can provide sufficient clues for PEComa diagnosis, which includes loosely cohesive, epithelioid morphology with abundant clear or eosinophilic cytoplasm, low-grade nuclear atypia, cytoplasmic melanin pigments. (biomedcentral.com)
  • Background: Perivascular epithelioid cell tumours (PEComas) are mesenchymal neoplasms with variable biological behaviour, ranging from benign to extremely aggressive diseases able to metastasize. (fortuneonline.org)
  • Diestelkamp T, Mikes Z, Wilson-Smith R, Germaine P. Radiological findings of two neoplasms with perivascular epithelioid cell differentiation. (jpccr.eu)
  • Merkel cell carcinoma (MCC), squamous cell carcinoma (SCC), pigmented epithelioid melanocytoma (PEM), and other rare skin neoplasms have a well-known risk to spread to regional lymph nodes. (hindawi.com)
  • Perivascular epithelioid cell tumors (PEComas) are a rare group of mesenchymal neoplasms characterized by the presence of histologically and immunohistochemically distinctive perivascular epithelioid cells [ 1 ], which can occur in any part of the body. (biomedcentral.com)
  • A family of mesenchymal tumors composed of histologically and immunohistochemically distinctive perivascular epithelioid cells. (curehunter.com)
  • The treatment options for mesothelioma epithelioid depend on the stage of the cancer, the location of the tumors, and the overall health of the patient. (mesothelioma.id)
  • The survival rate for mesothelioma epithelioid depends on several factors, including the stage of the cancer at diagnosis, the location of the tumors, and the overall health of the patient. (mesothelioma.id)
  • Malignant tumors with granulomatous change have sometimes been reported in the literature, but benign tumors with epithelioid granuloma , such as the present one, are rare. (karger.com)
  • Launch The perivascular epithelioid cell (PEC) is a cell type that's histologically and immunohistochemically within several tumors, including renal angiomyolipoma (AML), clear-cell glucose tumor (CCST) lymphangioleiomyomatosis (LAM), and rare clear-cell tumors of other anatomical sites. (cell-signaling-pathways.com)
  • Zamboni et al[4] asserted that obvious cell tumors of the lung arise from your perivascular epithelioid cell (PEC) and mentioned that related cells have been recognized in AML and lymphangiomyomas. (cell-signaling-pathways.com)
  • Renal epithelioid angiomyolipoma: a study of six cases and a meta-analytic study. (karger.com)
  • Histological variants of AML such as epithelioid angiomyolipoma (EAML) are considered to be locally aggressive. (bmj.com)
  • We report a case of a 17-year-old girl with tuberous sclerosis complex who underwent partial nephrectomy for a newly discovered 7.5-cm renal mass subsequently determined to be an epithelioid angiomyolipoma, a rare variant of angiomyolipoma that can be confused clinically, radiographically, and pathologically for renal cell carcinoma. (wustl.edu)
  • This case report and review of literature serve at increasing the awareness of this renal tumor, with its somewhat unpredictable outcome, reviewing the pertinent literature on the topic of epithelioid angiomyolipoma in the clinical setting of tuberous sclerosis complex. (wustl.edu)
  • The purpose of this study was to describe the imaging features of renal epithelioid angiomyolipoma (EAML), a rare subtype of angiomyolipoma, with clinical and pathologic correlation. (elsevierpure.com)
  • The present study aims to describe the radiological, clinicopathological, and immunohistochemical findings of a case of epithelioid angiosarcoma located in the posterior mediastinum of a 65-year-old male patient who underwent surgery and clinical treatment (Doxorubicin-based chemoterapy). (bvsalud.org)
  • We herein report a case of epithelioid GBM developing at the site of a left temporal PXA 13 years after the treatment of the primary tumor. (elsevierpure.com)
  • We present a case of epithelioid hemangioma of the penis in a 50-year-old Caucasian man. (biomedcentral.com)
  • Karska K, Kozioł I, Leśniewska M, Budzyńska J, Woźniak M. Radiological features of perivascular epithelioid cell tumours (PEComas) in a paediatric patient - Case report. (jpccr.eu)
  • Imaging features of primary and metastatic malignant perivascular epithelioid cell tumours. (jpccr.eu)
  • When in-depth testing is done, the rates of mesothelioma diagnosis actually increase, meaning many epithelioid mesothelioma victims avoid being misdiagnosed with related, but different, diseases. (mesothelioma-attorney.com)
  • Yes, there are several factors that can affect the 5-year survival rate for epithelioid mesothelioma, including age at diagnosis, tumor grade and size, stage at diagnosis, and treatment received. (meaningkosh.com)
  • Some steps that can be taken to improve one's chances of surviving epithelioid mesothelioma include seeing a specialist as soon as possible (ideally within six months of diagnosis), undergoing multimodal therapy (which combines surgery, radiation therapy and chemotherapy) if feasible, participating in clinical trials whenever possible and remaining positive throughout the course of treatment. (meaningkosh.com)
  • A patient's epithelioid mesothelioma diagnosis helps specialists determine the best treatment plan. (mesotheliomaguide.com)
  • In this article, we will delve into what epithelioid mesothelioma is, its symptoms, diagnosis, treatment options, and address some frequently asked questions surrounding this condition. (latmil.com)
  • Epithelioid hemangioma of the penis should be considered in the differential diagnosis of patients presenting with painful penile lumps. (biomedcentral.com)
  • A pathological diagnosis of epithelioid hemangioma was made. (biomedcentral.com)
  • This immunophenotype excluded a carcinoma, a lymphoid, melanocytic, germ cell, or neuroglial proliferation, and the diagnosis of sellar and suprasellar epithelioid angiosarcoma was made. (medscape.com)
  • Vascular markers allowed us in this case to make the unusual diagnosis of primary epithelioid angiosarcoma. (medscape.com)
  • The FDA has approved sirolimus protein-bound particles for injectable suspension (albumin-bound) (Fyarro™, Aadi Bioscience) for patients with locally advanced unresectable or metastatic malignant perivascular epithelioid cell tumor. (oncdata.com)
  • The multicenter, single-arm clinical trial enrolled 31 patients with locally advanced unresectable or metastatic malignant perivascular epithelioid cell tumor. (oncdata.com)
  • Nonmelanoma skin cancer with potential metastatic spreading to regional lymph nodes regroups skin lesions like high-risk squamous cell carcinoma (SCC), Merkel cell carcinoma (MCC), and pigmented epithelioid melanocytoma (PEM). (hindawi.com)
  • One patient had metastatic disease at presentation with epithelioid tumor identified in a single lymph node. (elsevierpure.com)
  • Perivascular epithelioid cell tumour: dynamic CT, MRI and clinicopathological characteristics-analysis of 32 cases and review of the literature. (jpccr.eu)
  • Zhao J, Teng H, Zhao R, Ding W, Yu K, Zhu L, Zhang J, Han Y. Malignant perivascular epithelioid cell tumour of the lung synchronous with a primary adenocarcinoma: one case report and review of the literature. (jpccr.eu)
  • Xuesong D, Hong G, Weiguo Z. Bladder Perivascular Epithelioid Cell Tumour: Dynamic CT and MRI Presentation of 2 Cases With 2-year Follow-up and Review of the Literature. (jpccr.eu)
  • Epithelioid angiosarcoma is a rare malignant neoplasm found in vascular endothelial cells. (bvsalud.org)
  • The histologic changes may be indistinguishable from conventional blue nevi or epithelioid blue nevi (EBN), a benign dermal-based melanocytic neoplasm with epithelioid morphology and heavily pigmented cytoplasm. (uky.edu)
  • ZFP36-FOSB fusion defines a subset of epithelioid hemangioma with atypical features. (uchicago.edu)
  • Epithelioid hemangioma is a rare vascular tumor found in the penis. (biomedcentral.com)
  • Epithelioid hemangioma is a rare vascular tumor that is characterized by capillary vessels lined by epithelioid endothelial cells and accompanied by an inflammatory cell infiltrate [ 1 - 4 ]. (biomedcentral.com)
  • A) Ultrasound picture shows the epithelioid hemangioma lesion on the dorsum of the penis. (biomedcentral.com)
  • Epithelioid hemangioma, first described in 1969, is a rare vascular lesion that typically arises on the head and distal extremities. (biomedcentral.com)
  • An open-label, multicenter, phase II study of bevacizumab for the treatment of angiosarcoma and epithelioid hemangioendotheliomas. (uchicago.edu)
  • Pathologic features of epithelioid angiosarcoma. (medscape.com)
  • Histologic evaluation of the thyroid nodule showed multinodular proliferation of oval to polygonal-shaped epithelioid cells with oval nuclei and eosinophilic cytoplasm arranged in sheet- or cord-like patterns, accompanied by fibrous stroma and marked osseous metaplasia. (springeropen.com)
  • The epithelioid cells had abundant eosinophilic cytoplasm with large nuclei and distinct central nucleoli (Figure 3 ). (biomedcentral.com)
  • Microscopically, some loosely cohesive epithelioid cells were uniform with abundant clear cytoplasm, showing predominantly round or oval nuclei with finely stippled chromatin. (biomedcentral.com)
  • Microscopically, we observed some loosely cohesive atypical cells arranged in single or clusters and sheets, which exhibited epithelioid morphology with abundant clear cytoplasm. (biomedcentral.com)
  • The cell block section showed single or clusters of medium-sized epithelioid cells in a background of fibrinoid fluid, with abundant clear or granular eosinophilic cytoplasm. (biomedcentral.com)
  • Histopathological examination revealed a well circumscribed, unencapsulated lesion (Figure 2 ) composed of central sheets of plump epithelioid cells with scattered vessels at the periphery. (biomedcentral.com)
  • There were scattered capillary vessels lined by epithelioid cells at the periphery of the lesion (Figure 4 ). (biomedcentral.com)
  • FISH analysis also revealed that, in 4 of 28 cases (14%), the AECC of the lesion demonstrated polyploidy localized to the large epithelioid cell component. (uky.edu)
  • Clinical trials involve testing new treatment options for mesothelioma epithelioid, including novel drugs, therapies, and surgical techniques. (mesothelioma.id)
  • Combined melanocytic nevi can contain a phenotypically distinct population of large atypical epithelioid cells in a background of smaller banal-appearing melanocytes. (uky.edu)
  • On the basis of the pattern of proliferation and degree of pigmentation, nevi with this pattern have been referred to as nevi with an atypical epithelioid cell component (N-AECC). (uky.edu)
  • This is likely more common among cases of N-AECC that have an atypical spitzoid epithelioid cell component, particularly those with obvious senescent nuclear changes. (uky.edu)
  • The expression of melanocytic markers is more frequently and strongly seen with epithelioid variant of AML . (webpathology.com)
  • Epithelioid mesothelioma treatment options vary depending on the patient's stage of cancer and type of mesothelioma. (mesotheliomaguide.com)
  • There are three surgery options for epithelioid mesothelioma treatment: extrapleural pneumonectomy (EPP), pleurectomy with decortication (P/D) and cytoreductive surgery with HIPEC. (mesotheliomaguide.com)
  • While there is currently no known cure for mesothelioma, including epithelioid mesothelioma, treatment options have improved over the years, offering better outcomes and extended life expectancy for patients. (latmil.com)
  • The most common treatment options for epithelioid mesothelioma are surgery, chemotherapy, immunotherapy and radiation. (mesotheliomaguide.com)
  • Treatment for malignant epithelioid mesothelioma typically involves surgery, radiation therapy, and chemotherapy. (quicktvafrica.com)
  • There are three main types of treatments for malignant epithelioid mesothelioma: surgery, radiation therapy, and chemotherapy. (quicktvafrica.com)
  • The primary treatment modalities for epithelioid mesothelioma include surgery, chemotherapy, and radiation therapy. (latmil.com)
  • Epithelioid pleural mesothelioma surgical options include extrapleural pneumonectomy (EPP) and pleurectomy with decortication (P/D). These procedures focus on removing the pleura, where pleural mesothelioma forms. (mesotheliomaguide.com)
  • This is particularly evident in prior studies of the pulmonary toxicity of single walled carbon nanotube s (SWCNT) where large granulomatous lesions encased by epithelioid macrophages were produced by large agglomerates of SWCNT (approximately 15 um diameter). (cdc.gov)
  • However, no granulomatous lesions or epithelioid macrophages were detected. (cdc.gov)
  • The initial tissue reaction to infection is a focal, intensely suppurative necrosis consisting largely of accumulations of polymorphonuclear leukocytes, followed by invasion of macrophages, epithelioid cells, and lymphocytes. (cdc.gov)
  • A final ultrasound-guided liver biopsy was performed and histology demonstrated epitheloid haemangioendothelioma, which was locally advanced and inoperable. (regsj.dk)
  • Epithelioid cells are associated with more aggressive behavior and carry a poorer prognosis for the patient's survival. (medscape.com)
  • Epithelioid: Cells look similar to normal mesothelial cells. (unityofscience.org)
  • Immunohistochemistry showed that the epithelioid cells were positive for CD34. (biomedcentral.com)
  • The epithelioid cells were uniform and approximately the same size as the parabasal cells (Fig. 1 A&B), showing predominantly round or oval nuclei with finely stippled chromatin. (biomedcentral.com)
  • A few spindled nuclei and melanin pigments were also identified (Fig. 2 A). IHC demonstrated that the epithelioid cells were positive for HMB45 andTFE3 (Fig. 2 B&C), focally positive for Melan-A, while negative for S-100, SOX-10, AE1/AE3, EMA, Desmin, SMA, H-caldesmon. (biomedcentral.com)
  • Suppurative lesions become granulomatous, and histopathological examination of the granulomas shows a central necrotic, sometimes caseating, zone surrounded by a layer of epithelioid cells, multinucleated giant cells, and fibroblasts in a radial arrangement, typical of other granulomatous conditions such as tuberculosis and sarcoidosis. (cdc.gov)
  • Malignant proliferation showing large monomorphic cells with some epithelioid (A1E/AE3) or angiocentric aspects without clear vascular differentiation. (medscape.com)
  • These findings suggest that epithelioid GBM may arise from a PXA with a BRAF V600E mutation. (elsevierpure.com)
  • Epithelioid mesothelioma is a type of malignant cancer that forms in the thin layer of tissue that covers most of our internal organs, known as the mesothelium. (meaningkosh.com)