Caroli disease (communicating cavernous ectasia, or congenital cystic dilatation of the intrahepatic biliary tree) is a rare inherited disorder characterized by cystic dilatation (or ectasia) of the bile ducts within the liver. (wikipedia.org)
They are both characterized by dilatation of the intrahepatic biliary tree. (medscape.com)
In 1958 Jacques Caroli described communicating cavernous ectasia of the biliary tree as an uncommon cause of chronic, often life-threatening hepatobiliary disease. (qxmd.com)
Caroli disease also is known as communicating cavernous ectasia or congenital cystic dilatation of the intrahepatic biliary tree. (medscape.com)
The most common, and often the first, interventional radiologic procedure is PTC, which reveals dilated segmental intrahepatic biliary radicles. (medscape.com)
Caroli disease is distinct from other diseases that cause ductal dilatation caused by obstruction, in that it is not one of the many choledochal cyst derivatives. (wikipedia.org)
This is a rare congenital disorder that classically causes saccular ductal dilatation, which usually is segmental. (medscape.com)
It is distinct from other diseases that cause ductal dilatation caused by obstruction. (medscape.com)
Intrahepatic7
Images taken by CT scan, X-ray, or MRI show enlarged intrahepatic (in the liver) bile ducts due to ectasia. (wikipedia.org)
The term Caroli disease is applied if the disease is limited to ectasia or segmental dilatation of the larger intrahepatic ducts. (medscape.com)
In Caroli disease, abnormalities of the bile duct occur at the level of the large intrahepatic ducts (ie, left and right hepatic ducts, segmental ducts), resulting in dilatation and ectasia. (medscape.com)
The disease now most often referred to as Caroli's disease is a rare condition characterized by nonobstructive saccular or fusiform dilatation of the intrahepatic bile ducts. (qxmd.com)
Caroli disease is a nonobstructive dilatation of the intrahepatic bile ducts, which was first described in 1958 by the French physician Jacques Caroli. (medscape.com)
Nuclear scintigraphy also may be performed in the initial workup and can be valuable in excluding obstructive causes for intrahepatic duct dilatation that are depicted on cross-sectional images. (medscape.com)
With PTC or ERCP, the diagnosis can be made with a high degree of confidence when the large intrahepatic branches have focal or segmental involvement with cystic outpouchings in which the contrast medium collects. (medscape.com)
Drawing shows the main right hepatic duct and the multiple segmental branch dilatations related to Caroli disease. (medscape.com)
Focal segmental1
Renal scarring causes renal hypertension, proteinuria, focal segmental glomerular sclerosis, and growth delay and may lead to terminal renal insufficiency (see chronic pyelonephritis ). (urology-textbook.com)
Annuloaortic ectasia2
kappa 0.Eighty three): supratubal aneurysm (20 sufferers), aortic main aneurysm (Several), along with annuloaortic ectasia (24). (autophagysignal.com)
For example, many patients with Marfan syndrome and annuloaortic ectasia are suitable for valve-sparing aortic root replacement, which obviates the need for a life-long anticoagulation regimen. (bcm.edu)
Saccular2
In the so-called pure form, dilatation is classically segmental and saccular and is associated with stone formation and recurrent bacterial cholangitis. (qxmd.com)
Note the saccular dilatations that can occur, involving the right lobe of liver in this case. (medscape.com)
This process can be either diffuse or segmental and may be limited to one lobe of the liver, more commonly the left lobe. (medscape.com)
Background: Coronary artery ectasia (CAE), known for localized or diffuse excessive dilatation of the coronary artery, has an unknown etiology, but it has been reported that the underlying cause may be atherosclerosis and genetic changes that may affect the arterial lumen. (bvsalud.org)
Saccular dilatations2
The disease consists of segmental, saccular dilatations of the bile ducts. (medscape.com)
Note the saccular dilatations that can occur, involving the right lobe of liver in this case. (medscape.com)
Cystic dilatation3
Caroli disease (communicating cavernous ectasia, or congenital cystic dilatation of the intrahepatic biliary tree) is a rare inherited disorder characterized by cystic dilatation (or ectasia) of the bile ducts within the liver. (wikipedia.org)
1, 2, 3] Caroli disease also is known as communicating cavernous ectasia or congenital cystic dilatation of the intrahepatic biliary tree. (medscape.com)
Pancreatic divisum can result in a santorinicele 2 , which is a cystic dilatation of the distal dorsal duct, immediately proximal to the minor papilla. (radiopaedia.org)
Intrahepatic biliary tree1
They are both characterized by dilatation of the intrahepatic biliary tree. (medscape.com)
Congenital3
This is a rare congenital disorder that classically causes saccular ductal dilatation, which usually is segmental. (medscape.com)
In Caroli disease, abnormalities of the bile duct occur at the level of the large intrahepatic ducts (ie, left and right hepatic ducts, segmental ducts), resulting in dilatation and ectasia. (medscape.com)
Biliary tract1
In the liver, increased hepatic fibrosis often associates with cysts lined with biliary epithelium and a variable degree of intrahepatic biliary tractdilatation. (bmj.com)
Bile2
Images taken by CT scan, X-ray, or MRI show enlarged intrahepatic (in the liver) bile ducts due to ectasia. (wikipedia.org)
One of the manifestations that has received intensive study are related to the ductal plate malformation of the liver and comprise proliferation and dilatation of the intrahepatic bile ductules, with a variable degree of fibrosis and cyst formation. (bmj.com)
Commonly3
Fibromuscular dysplasia most commonly causes small stenoses along a vessel with intervening areas of dilatation (small aneurysms), creating a "string of beads" appearance. (radiopaedia.org)
For the NME lesion, the segmental or regional distribution was more commonly observed in the papilloma with high-risk or malignant lesions (61.5%) than the benign papilloma (12.5%) ( P = 0.006). (biomedcentral.com)
When segmental, it most commonly affects the corpus cauda junction. (nih.gov)
Abnormal4
The changes include the proliferation and dilatation of epithelial ducts in these tissues with abnormal deposition of extracellular matrix. (bmj.com)
for ANABOLIC STEROID use TESTOSTERONE CONGENERS 2017-2022 BX - Anabolic Androgenic Steroid BX - Anabolic Steroid MH - Aneurysm, Aortic Arch UI - D000094626 MN - C14.907.55.239.125.250 MN - C14.907.109.139.125.250 MS - An abnormal balloon- or sac-like dilatation in the wall of the AORTIC ARCH. (nih.gov)
HN - 2023 BX - Aortic Arch Aneurysm MH - Aneurysm, Ascending Aorta UI - D000094625 MN - C14.907.55.239.125.500 MN - C14.907.109.139.125.500 MS - An abnormal balloon- or sac-like dilatation in the wall of the ASCENDING AORTA. (nih.gov)
HN - 2023 BX - Anti-Racism FX - Racism MH - Aortic Aneurysm, Thoracoabdominal UI - D000094624 MN - C14.907.55.239.75.500 MN - C14.907.109.139.75.500 MS - An abnormal balloon- or sac-like dilatation in the wall of ABDOMINAL AORTA at the aortic hiatus. (nih.gov)
Gastric antral vascular ectasia (GAVE), also known as "Watermelon stomach", is a rare cause of upper gastrointestinal bleeding (UGIB). (bvsalud.org)
Include2
They include the proliferation and dilatation of epithelial ducts, and proliferative changes in the extracellular matrix of stromal connective tissue. (bmj.com)
Subtle findings can include increased renal size, ureteral dilatation, perinephric hematoma, and renal infarction. (medscape.com)
Areas1
In crescentic GN, segmental areas of visceral or parietal cells form adhesions to one another and reduce Bowman's space. (nih.gov)
Common2
The most common, and often the first, interventional radiologic procedure is PTC, which reveals dilated segmental intrahepatic biliary radicles. (medscape.com)
The characteristic finding, particularly in the more common medial subtype, is alternating stenoses and dilatations, causing a string of beads appearance 5 . (radiopaedia.org)