• Superior mesenteric artery (SMA) syndrome is a gastro-vascular disorder in which the third and final portion of the duodenum is compressed between the abdominal aorta (AA) and the overlying superior mesenteric artery. (wikipedia.org)
  • Superior mesenteric artery (SMA) syndrome is an uncommon but well recognized clinical entity characterized by compression of the third, or transverse, portion of the duodenum between the aorta and the superior mesenteric artery. (medscape.com)
  • The superior mesenteric artery usually forms an angle of approximately 45° (range, 38-56°) with the abdominal aorta, and the third part of the duodenum crosses caudal to the origin of the superior mesenteric artery, coursing between the superior mesenteric artery and aorta. (medscape.com)
  • Any factor that sharply narrows the aortomesenteric angle to approximately 6-25° can cause entrapment and compression of the third part of the duodenum as it passes between the superior mesenteric artery and aorta, resulting in SMA syndrome. (medscape.com)
  • It" was superior mesenteric artery syndrome, or SMAS, which occurs when the duodenum is compressed between two arteries-the aorta and superior mesenteric artery-resulting in partial or complete blockage of the duodenum. (hopkinsmedicine.org)
  • When patients have compression of the duodenum, between the aorta posteriorly and the superior mesenteric artery (SMA) anteriorly, which is known as SMA syndrome, a succussion splash also may be evident. (medscape.com)
  • It results from obstruction of the third portion of the duodenum due to the narrowing of the angle between the abdominal aorta and superior mesenteric artery. (boneandspine.com)
  • Background: Superior Mesenteric Artery Syndrome (SMA syndrome) is a condition that occurs when the third part of the duodenum is compressed between the Aorta and the Superior Mesenteric Artery which causes postprandial abdominal pain, nausea, and vomiting due to partial or complete blockage of the duodenum. (journalcra.com)
  • Superior mesenteric artery syndrome (SMA syndrome) or Wilkie's syndrome is a rare etiology of duodenal obstruction due to compression of the third portion of the duodenum between the superior mesenteric artery and the aorta. (ejcrim.com)
  • Nutcracker syndrome is a vascular compression disorder that refers to the compression of the left renal vein, most commonly between the superior mesenteric artery (SMA) and aorta , although other variations can exist 1 . (radiopaedia.org)
  • A barium swallow X-ray with small bowel follow-through and computed tomography scan demonstrated remarkable duodenal narrowing between the superior mesenteric artery and the aorta, consistent with superior mesenteric artery syndrome. (biomedcentral.com)
  • The small bowel obstruction occurred as a result of weight loss secondary to the anorexia, which then led to loss of the omental fat pad and consequent compression of the duodenum between the superior mesenteric artery (SMA) and the aorta. (biomedcentral.com)
  • SMA syndrome is generally felt to result from compression of the duodenum between the superior mesenteric artery anteriorly/dorsally and the aorta (and behind the aorta, the vertebral column) posteriorly/ventrally [ 4 ]. (biomedcentral.com)
  • In the absence of an appropriate fatty scaffolding, the angle at which the SMA branches from the aorta is reduced resulting in compression of the third portion of the duodenum between the SMA and the aorta [ 4 ]. (biomedcentral.com)
  • There was compression of D3 (third part of duodenum) between the aorta and SMA ( Figs. 1 and 2 ). (journalmc.org)
  • SMA syndrome, also known as aortomesenteric duodenal compression or duodenal vascular compression or Wilkie's syndrome or Cast syndrome, is a rare clinical entity that results from the compression of the third part of the duodenum as it passes between the overlying SMA and the aorta [ 1 ]. (journalmc.org)
  • it is of varying size and is wedged between the superior mesenteric vessels (vein on the right, artery on the left) in front and the aorta behind it. (medscape.com)
  • Symptoms are caused by compression of the third portion of the duodenum by the SMA. (sages.org)
  • Superior mesenteric artery (SMA) syndrome is an uncommon disease resulting from compression and partial obstruction of the third portion of the duodenum from the SMA. (bvsalud.org)
  • Abdominal CT showed a narrowed third portion of the duodenum, with a distended stomach and proximal duodenum. (bvsalud.org)
  • Kyslan K, Barla J, Kyslan K, Stanislayova M. [Superior mesenteric artery (SMAS/AMS) syndrome and its management]. (medscape.com)
  • Surgeries to treat SMAS include the Strong's procedure, in which the duodenum is re-positioned to the right of the superior mesenteric artery, and gastrojejunostomy, in which the jejunum is joined directly to the stomach. (hopkinsmedicine.org)
  • Although Toprak was unaware of it at the time, she was suffering from Wilkie's syndrome - a.k.a. superior mesenteric artery syndrome (SMAS). (com.pk)
  • Thankful to be alive, she now wants to warn others about Superior Mesenteric Artery Syndrome (SMAS), also Known as Wilkie's disease. (itv.com)
  • SMAS is a condition of the digestive system which affects fewer than one per cent of the population and occurs when part of the small intestine is compressed between two arteries, causing a partial or complete blockage. (itv.com)
  • The acute form of SMA syndrome develops rapidly after traumatic incidents that forcibly hyper-extend the SMA across the duodenum, inducing the obstruction, or sudden weight loss for any reason. (wikipedia.org)
  • [ 1 ] Superior mesenteric artery syndrome was first described in 1861 by Von Rokitansky, who proposed that its cause was obstruction of the third part of the duodenum as a result of arteriomesenteric compression. (medscape.com)
  • Baltazar U, Dunn J, Floresguerra C. Superior mesenteric artery syndrome: an uncommon cause of intestinal obstruction. (medscape.com)
  • Superior mesenteric artery (SMA) syndrome is an atypical, rare cause of both acute and chronic high intestinal obstruction secondary to extrinsic vascular compression. (sages.org)
  • Acute colonic pseudo obstruction (Ogilvie's syndrome): case report. (ac.ke)
  • Case presentation: We report an original case of a previously diagnosed 35-year-old female with SMA syndrome through history and radiological findings who initially underwent gastrojejunostomy for the treatment of her SMA syndrome two years prior to her presentation without resolution of her gastric outlet obstruction symptoms. (journalcra.com)
  • While superior mesenteric artery syndrome is an uncommon cause of small bowel obstruction, the general pediatrician and child psychiatrist should be aware of this complication of anorexia nervosa. (biomedcentral.com)
  • Duodenal obstruction by compression from the superior mesenteric artery (SMA) can be managed using minimally invasive techniques. (journalmc.org)
  • Retroperitoneal fat and lymphatic tissue normally serve as a cushion for the duodenum, protecting it from compression by the SMA. (wikipedia.org)
  • citation needed] Patients with the chronic, congenital form of SMA syndrome predominantly have a lengthy or even lifelong history of abdominal complaints with intermittent exacerbations depending on the degree of duodenal compression. (wikipedia.org)
  • Alternatively, other causes implicated in superior mesenteric artery syndrome include high insertion of the duodenum at the ligament of Treitz, a low origin of the superior mesenteric artery, and compression of the duodenum due to peritoneal adhesions. (medscape.com)
  • Upon her visit, Scholbach diagnosed Toprak with three compression syndromes in addition to Wilkie's syndrome: nutcracker syndrome, Dunbar syndrome, and May-Thurner syndrome. (com.pk)
  • In Germany, Scholbach gave Toprak what's called an SMA transposition - the removal of the compressing SMA, which avoids contact and compression of the duodenum. (com.pk)
  • Nutcracker syndrome should not be confused with superior mesenteric artery syndrome (Wilkie syndrome), also a superior mesenteric artery compression disorder , where the SMA compresses the third part of the duodenum (the two conditions, however, may be associated). (radiopaedia.org)
  • This compression causes partial or complete blockage of the duodenum. (itv.com)
  • This compression results from the loss of fatty tissue, which surrounds the superior mesenteric artery and its neurovascular pedicle. (biomedcentral.com)
  • A subsequent barium meal and follow-through demonstrated a linear compression at the third part of the duodenum causing dilation of the proximal duodenum. (journalmc.org)
  • Compression of the left common ILIAC VEIN by the right common ILIAC ARTERY against the underlying fifth LUMBAR VERTEBRA is the typical underlying malformation. (lookformedical.com)
  • [ 2 ] Nevertheless, extended survival was seen in a few patients and included a 3-year-old girl who received a multivisceral transplant (stomach, duodenum, pancreas, small bowel, colon and liver). (medscape.com)
  • The pancreas lies in the curve of the duodenum and controls the level of sugar in the blood by secreting insulin and glucagon. (medscape.com)
  • The pancreas is prismoid in shape and appears triangular in cut section, with superior, inferior, and anterior borders as well as anterosuperior, anteroinferior, and posterior surfaces. (medscape.com)
  • Duodenum and pancreas. (medscape.com)
  • The sphincter of Oddi is a muscular valve that controls the flow of digestive juices (bile and pancreatic juice) through ducts from the liver and pancreas into the first part of the small intestine (duodenum). (iffgd.org)
  • bile from the liver and secretions from the pancreas come through the ampulla of Vater to mix with food in the duodenum and aid digestion. (letswinpc.org)
  • The common bile duct then courses downward about 7 cm, passes behind the superior part of the duodenum, and enters the pancreas. (clinicalgate.com)
  • It has three areas called the duodenum, the ileum, and the jejunum. (medlineplus.gov)
  • Upper gastrointestinal endoscopy performed with a colonoscope revealed active bleeding from a metastatic tumour involving the duodenum and the proximal jejunum. (ispub.com)
  • The diseased part of the small intestine (ileum or duodenum or jejunum) is removed. (surgeryencyclopedia.com)
  • SMA syndrome is also known as Wilkie's syndrome, cast syndrome, mesenteric root syndrome, chronic duodenal ileus and intermittent arterio-mesenteric occlusion. (wikipedia.org)
  • It took an MRI, colonoscopy, and endoscopy to discover she had Wilkie's syndrome. (com.pk)
  • Eventually, she found a publication authored by a German doctor named Thomas Scholbach who specializes in gastrointestinal conditions like Wilkie's syndrome. (com.pk)
  • According to Dr. Mark Taylor, central zone executive medical director of the Nova Scotia Health Authority, "the diagnosis [for Wilkie's syndrome] is quite simple with a CT scan in most cases. (com.pk)
  • But, as Toprak experienced firsthand, Wilkie's syndrome can worsen without a proper - and fast - diagnosis. (com.pk)
  • Taylor told CBC that vascular surgeons in Nova Scotia, for example, don't recommend it for Wilkie's syndrome as it is a "much bigger and more dangerous operation. (com.pk)
  • Risk factors include anatomic characteristics such as: asthenic (very thin or "lanky") body build, an unusually high insertion of the duodenum at the ligament of Treitz, a particularly low origin of the SMA, or intestinal malrotation around an axis formed by the SMA. (wikipedia.org)
  • To evaluate the role of laparosopic lysis of the ligament of Treitz as a less invasive option in the presence of SMA syndrome that does not improves with medical treatment. (sages.org)
  • We believe that laparoscopic lysis of the ligament of Treitz is a good option for treatment of SMA syndrome because it has a 75% success rate, spares the patient of an anastomosis and in the cases where it fails more invasive procedures like gastrojejunostomy or duodenojejunostomy can be safely performed. (sages.org)
  • When that fat is reduced by severe weight loss, the angle of the SMA takeoff is diminished and it obstructs the duodenum as it transits up toward the ligament of Treitz. (medscape.com)
  • The duodenum, the first portion of the small bowel, is a C-shaped structure that lies at the level of the L1 to L3 vertebrae and extends from the gastric pylorus to the ligament of Treitz. (myesr.org)
  • CT scan of abdomen showed dilatation of stomach, first and second part of duodenum. (journalmc.org)
  • An endoscope is a thin, flexible tube with a light and a lens on the end used to look into the esophagus, stomach, duodenum, small intestine, colon, or rectum. (iffgd.org)
  • Predominant arterial blood supply of stomach is through Left gastric artery. (medicosplexus.com)
  • And has two flexures, the superior and the inferior duodenal flexures. (myesr.org)
  • the inferior mesenteric vein empties into the splenic vein, the superior mesenteric vein joins the splenic vein to form the portal vein. (lookformedical.com)
  • Parts of Mesorectal fascia includes Superior rectal vein, pararectal nodes and inferior mesenteric plexus and doesn't include Inferior rectal vein. (medicosplexus.com)
  • Blood supply to medulla includes Anterior spinal artery, Posterior inferior cerebellar artery but does not include Superior cerebellar. (medicosplexus.com)
  • It is covered by peritoneum over its inferior aspect, but it is directly apposed to the surface of the liver along its superior aspect. (clinicalgate.com)
  • It is distinct from nutcracker syndrome, which is the entrapment of the left renal vein between the AA and the SMA, although it is possible to be diagnosed with both conditions. (wikipedia.org)
  • In certain situations, the syndrome can result from a retroaortic or circumaortic left renal vein . (radiopaedia.org)
  • Although innumerable details of pancreaticoduodenectomy yield to continued innovation, a comprehensive discussion of intraoperative variants (ie, duct to mucosa vs invagination of the pancreaticojejunal anastomosis, diverse approaches to vein resection and reconstructions, nuances of each enteric anastomosis, and modifications of Roux-en-Y reconstructions, to name a few) is beyond the scope of this article. (medscape.com)
  • A short thick vein formed by union of the superior mesenteric vein and the splenic vein. (lookformedical.com)
  • Intercostal space which doesn't follow VAN (Vein, Artery and Nerve) structure is 1st intercostal space. (medicosplexus.com)
  • The common bile duct is the most anterior structure of the three major structures of the porta hepatis: common bile duct, portal vein, and hepatic artery. (clinicalgate.com)
  • There may be marked variation in the relationship of the biliary tree to the portal vein and hepatic artery where these structures approach the porta hepatis and enter the liver. (clinicalgate.com)
  • This rare, potentially life-threatening syndrome is typically caused by an angle of 6-25° between the AA and the SMA, in comparison to the normal range of 38-56°, due to a lack of retroperitoneal and visceral fat (mesenteric fat). (wikipedia.org)
  • The duodenum is mostly retroperitoneal in location, except. (myesr.org)
  • Staging of the disease followed by CAT scanning of the upper and lower abdomen and of the retroperitoneal space showed multiple, enlarged bilateral para-aortic, and mesenteric lymph nodes. (ispub.com)
  • Seventeenth-century English anatomist William Harvey, who questioned some of Galen's conclusions, described the heart as a 4-chambered pump that moves blood through arteries and veins, not air. (medscape.com)
  • Neoplasms located in the vasculature system, such as ARTERIES and VEINS. (lookformedical.com)
  • As bacteria proliferate and more gas is produced, the intraluminal gas may dissect into the necrotic wall (pneumatosis intestinalis), spread through the mesenteric veins, and finally flow into the portal veins (Fig. 7A , 7B ). (ajronline.org)
  • Most patients with mesenteric lesions present with non-specific symptoms of abdominal pain, tenderness, palpable abdominal swelling, abdominal distension and weight loss. (sajr.org.za)
  • Delay in the diagnosis of SMA syndrome can result in malnutrition , dehydration , electrolyte abnormalities, gastric pneumatosis and portal venous gas, formation of an obstructing duodenal bezoar, hypovolemia secondary to massive GI hemorrhage, and even death secondary to gastric perforation. (medscape.com)
  • In 1946, Waugh and Clagett described a formal en-bloc resection of the gallbladder with the common bile duct (CBD), gastric antrum, duodenum, and pancreatic head performed as a one-stage procedure, which we recognize today as the classic pancreaticoduodenectomy. (medscape.com)
  • Ultrashort bowel syndrome (USBS) is a group of heterogeneous disorders where the length of small bowel is less than 10 cm or 10% of expected for the age. (bmj.com)
  • Haemorrhage as a first presentation of small bowel metastases is extremely rare and is related to very poor patient survival especially when these are located in the duodenum. (ispub.com)
  • Interestingly, the most common cause is an eating disorder that leads to the loss of fatty tissue that surrounds the mesenteric artery, although anatomic abnormalities can also play a role. (hopkinsmedicine.org)
  • The middle meningeal artery is typically the third branch of the first part of the maxillary artery, one of the two terminal branches of the external carotid artery. (passmed.uk)
  • One-year survival has been reported following transplantation of a living-related segment of a donor intestine [ 4 ] and in a 41-year-old woman with short gut syndrome (SGS) secondary to superior mesenteric artery thrombosis. (medscape.com)
  • The patient underwent computed tomography enterography and its findings were consistent with SMA syndrome. (ejcrim.com)
  • The purpose of this exhibit is to present a graphical review of the anatomy of the duodenum and a series of compelling cases depicting the pathology of the duodenum (congenital, inflammatory, neoplastic, vascular, and iatrogenic disease) with their imaging characteristics at computed tomography (CT) studies. (myesr.org)
  • The aim of this article is to describe the spectrum of imaging findings of the various mesenteric lesions using ultrasound and CT. (sajr.org.za)
  • Knowledge of imaging characteristics of various mesenteric lesions helps in timely diagnosis and management. (sajr.org.za)
  • These symptoms are shared by pathologies of other abdominal organs and it is therefore very difficult to identify mesenteric lesions clinically. (sajr.org.za)
  • Understanding the characteristic radiological patterns on ultrasound (USG) and CT offers valuable insights for differential diagnoses of mesenteric lesions and their treatment. (sajr.org.za)
  • We got the CT scan and it was convincing for the radiologist that it was an anatomic problem and for us that surgery was reasonable," he adds, noting that Gabrielle's mesenteric artery was sharply angled and pinching off her duodenum, blocking the passage of food. (hopkinsmedicine.org)
  • ANATOMIC LANDMARKS OF THE DUODENUM Anatomical landmarks of the duodenum: the duodenum is divided into four segments and extends to both retro and intraperitoneal spaces. (myesr.org)
  • Anatomic relationships of the third duodenal segment: Anterior: superior. (myesr.org)
  • Nutcracker syndrome is slightly more common in females. (radiopaedia.org)
  • The most common clinical manifestations of nutcracker syndrome are left flank pain, pelvic pain, hematuria, and gonadal varices. (radiopaedia.org)
  • The first clinical report of this syndrome was made by El-Sadr and Mina in 1950 while the term "nutcracker syndrome" is thought to have been first used by de Schepper in 1972 7 . (radiopaedia.org)
  • 1. Kurklinsky A & Rooke T. Nutcracker Phenomenon and Nutcracker Syndrome. (radiopaedia.org)
  • It combines the use of x-rays and an endoscope that is passed down to the duodenum, where the bile duct and pancreatic ducts drain, and a dye that is injected into the ducts. (iffgd.org)
  • SMA syndrome usually occurs in older children and adolescents. (medscape.com)
  • It's a gastrointestinal condition that occurs when the first part of the small intestine - the duodenum - is compressed between two arteries, which causes its partial or complete blockage. (com.pk)
  • Superior mesenteric artery (SMA) syndrome is an interesting phenomenon that occurs when the SMA compresses the third part of the duodenum. (journalmc.org)
  • It usually occurs in patients with familial adenomatous polyposis (FAP) or Gardner syndrome. (sajr.org.za)
  • We report an original case of persistent SMA syndrome post gastrojejunostomy which was treated with laparoscopic revision of gastrojejunostomy followed by duodenojejunostomy with Roux-en-Y jejuenojejunostomy. (journalcra.com)
  • However, a narrow SMA angle alone is not enough to make a diagnosis, because patients with a low BMI, most notably children, have been known to have a narrow SMA angle with no symptoms of SMA syndrome. (wikipedia.org)
  • Despite multiple case reports, there has been controversy surrounding the diagnosis and even the existence of SMA syndrome since symptoms do not always correlate well with radiologic findings, and may not always improve following surgical correction. (wikipedia.org)
  • One year later, his twin brother also presented similar symptoms and was radiologically diagnosed as SMA syndrome. (keyopinionleaders.com)
  • Laparoscopic revision of gastro-jejunostomy followed by duodenojejunostomy with Roux-en-Y jejuenojejunostomy was successfully performed with resolution of the patient's symptoms. (journalcra.com)
  • The syndrome cannot be diagnosed by x-ray alone and the signs and symptoms can vary greatly from one person to another, so doctors must go through a process of excluding other causes first. (itv.com)
  • citation needed] SMA syndrome is usually difficult to differentiate with anorexia nervosa. (wikipedia.org)
  • Patients with SMA syndrome can be hindered restoring weight in those with anorexia nervosa. (wikipedia.org)
  • Nonetheless, the entity (also called cast syndrome) is a well-known complication of scoliosis surgery, anorexia, and trauma. (medscape.com)
  • To the best of our knowledge, there have been no previous publications detailing successful management of a patient with anorexia nervosa and superior mesenteric artery syndrome. (biomedcentral.com)
  • This case illustrates important points regarding the pathogenesis of superior mesenteric artery syndrome in the setting of anorexia, and it highlights the complexities that arise when managing an adolescent with both medical and psychiatric needs, as well as outlining a viable solution. (biomedcentral.com)
  • We therefore describe various treatment options for managing both anorexia and SMA syndrome, and illustrate how we utilized a variety of resources to develop a novel and appropriate care strategy for this patient. (biomedcentral.com)
  • In our patient, SMA syndrome resulted from weight loss associated with anorexia nervosa. (biomedcentral.com)
  • For Gabrielle, Garcia recommended a novel, less-invasive approach called laparoscopic duodenojejunostomy, during which-through three tiny incisions-the surgeon makes the small intestine bypass the duodenum. (hopkinsmedicine.org)
  • In some cases of SMA syndrome, severe malnutrition accompanying spontaneous wasting may occur. (wikipedia.org)
  • Conclusion: Surgical intervention is the mainstay in cases of SMA syndrome refractory to conservative management. (journalcra.com)
  • Laparoscopic treatment is feasible for the treatment of SMA syndrome given its safety and minimal invasiveness. (bvsalud.org)
  • SMA syndrome is thus considered only after patients have undergone an extensive evaluation of their gastrointestinal tract including upper endoscopy, and evaluation for various malabsorptive, ulcerative and inflammatory intestinal conditions with a higher diagnostic frequency. (wikipedia.org)
  • There is an increase in number of children with ultrashort bowel syndrome (USBS) being managed by intestinal rehabilitation services and they form nearly a quarter of children with short bowel syndrome. (bmj.com)
  • In a review of the literature, approximately 0.013-0.78% of the findings from upper GI tract barium studies support a diagnosis of superior mesenteric artery syndrome. (medscape.com)
  • The primary physical findings in classic Ramsay Hunt syndrome include peripheral facial nerve paresis with associated rash or herpetic blisters in the distribution of the nervus intermedius. (blogspot.com)
  • Some mesenteric diseases present with distinctive imaging findings while others have similar findings, thereby complicating their differential diagnosis. (sajr.org.za)
  • The hepatic artery and peripheral nerves lie most posteriorly. (clinicalgate.com)
  • [ 2 ] Approximately 0.013-0.78% of barium upper GI studies evaluating for superior mesenteric artery syndrome support the diagnosis. (medscape.com)
  • Merrett ND, Wilson RB, Cosman P, Biankin AV. Superior mesenteric artery syndrome: diagnosis and treatment strategies. (medscape.com)
  • Lippl F, Hannig C, Weiss W, Allescher H-D, Classen M, Kurjak M. Superior mesenteric artery syndrome: diagnosis and treatment from the gastroenterologist's view. (ejcrim.com)
  • CT plays an essential role in the diagnosis of mesenteric disease. (sajr.org.za)
  • Secondary involvement of the mesentery from tumours elsewhere is much more common than primary mesenteric neoplasms such as desmoid tumour, inflammatory myofibroblastic tumour (IMFT), and others. (sajr.org.za)
  • Endoscopy of the upper gastrointestinal tract up to the secondpart of the duodenum revealed erosive antral gastritis without an active bleeding site. (ispub.com)
  • Short bowel syndrome (SBS) is a reduction in functioning bowel length. (bmj.com)
  • After branching off the maxillary artery in the infratemporal fossa, it runs through the foramen spinosum to supply the dura mater and the calvaria. (passmed.uk)
  • Primary mesenteric solid neoplasms are rare and the majority of them are benign. (sajr.org.za)
  • [1] Other, less common causes include tobacco smoking , stress as a result of other serious health conditions, Behçet's disease , Zollinger-Ellison syndrome , Crohn's disease , and liver cirrhosis . (wikizero.com)
  • The liver is found in the superior right quadrant of the abdomen and weighs approximately 1.5 kilograms. (lecturio.com)
  • Low hepatic ATP, hyperuricemia, and hepatic lipid accumulation reported in metabolic syndrome (MetS) patients may reflect insufficient hepatic O 2 delivery, potentially accounting for the sympathetic overdrive associated with MetS. (surgicalneurologyint.com)