Motor Neuron DiseaseMuscular Atrophy, SpinalMotor NeuronsNeuromuscular DiseasesSpinal Muscular Atrophies of ChildhoodBulbar Palsy, ProgressiveSurvival of Motor Neuron 1 ProteinMuscular Dystrophy, DuchenneSMN Complex ProteinsSpinal CordSurvival of Motor Neuron 2 ProteinAmyotrophic Lateral SclerosisMuscular AtrophyAtrophyNeuronsMuscular Disorders, AtrophicBulbo-Spinal Atrophy, X-LinkedAnterior Horn CellsMuscular DystrophiesDystrophinNerve DegenerationNerve Tissue ProteinsSpinal Cord InjuriesAxonsSpinal Cord DiseasesFasciculationSuperoxide DismutaseNeuronal Apoptosis-Inhibitory ProteinDisease Models, AnimalDEAD Box Protein 20ElectromyographyCyclic AMP Response Element-Binding ProteinRNA-Binding ProteinsMotor CortexMuscle, SkeletalNeurons, AfferentNeurofilament ProteinsMice, TransgenicGaggingMice, Inbred mdxNeural ConductionTDP-43 ProteinopathiesInclusion BodiesFrontotemporal Lobar DegenerationFrontotemporal DementiaMotor ActivityMutationEvoked Potentials, MotorNeuromuscular JunctionSpinal Nerve RootsMuscular Dystrophy, AnimalToxascariasisbeta-Hexosaminidase beta ChainRNA-Binding Protein FUSRiluzoleUlnar NerveBrainPharyngostomyPyrrolidonecarboxylic AcidElectric InjuriesPedigreeDeglutition DisordersPick Disease of the BrainPeripheral NervesMusclesMuscle WeaknessBrain Injury, ChronicAction PotentialsLathyrismPhenotypeExonsHeterozygote DetectionRibonucleoproteins, Small NuclearNeurologic ExaminationImmunohistochemistryUtrophinSandhoff DiseaseRats, TransgenicMarchiafava-Bignami DiseaseParalysisReceptors, AndrogenDementiaMice, Inbred C57BLAxonal TransportAge of OnsetCells, CulturedElectric StimulationCricoid CartilageOptic AtrophyTime FactorsDNA Repeat ExpansionRecruitment, NeurophysiologicalAnimals, Genetically ModifiedSpinal NervesMagnetic Resonance ImagingCoiled BodiesDisease ProgressionInjections, SpinalGanglia, SpinalMice, Knockout