Motor NeuronsNeuronsMotor Neuron DiseaseHeavy Chain DiseaseMetallochaperonesSurvival of Motor Neuron 1 ProteinCation Transport ProteinsMachado-Joseph DiseaseNeurons, AfferentNerve Tissue ProteinsCell SurvivalSurvival of Motor Neuron 2 ProteinMotor CortexSurvival RateCopperEvoked Potentials, MotorHepatolenticular DegenerationAmyotrophic Lateral SclerosisSpinal Cord CompressionHeredodegenerative Disorders, Nervous SystemAnimals, CongenicMuscular Atrophy, SpinalMotor ActivityMenkes Kinky Hair SyndromeNeurodegenerative DiseasesAxonsSMN Complex ProteinsMutationImmunoglobulin gamma-ChainsAction PotentialsMice, TransgenicDisease-Free SurvivalCells, CulturedNuclear ProteinsPeptidesTime FactorsSurvivalInclusion BodiesHuntington DiseaseDisease Models, AnimalCarrier ProteinsMolecular Motor ProteinsNerve DegenerationElectric StimulationMolecular Sequence DataSynapsesMolecular ChaperonesNeuromuscular DiseasesGanglia, InvertebrateImmunohistochemistryProtein BindingProteostasis DeficienciesSurvival AnalysisElectrophysiologyAmino Acid SequenceSpinocerebellar AtaxiasInterneuronsSynaptic TransmissionGraft SurvivalCell LineRepressor ProteinsMovementCholinergic NeuronsSuperoxide DismutaseAplysiaDopaminergic NeuronsUbiquitinElectromyographyAnterior Horn CellsNeuromuscular JunctionDendritesSensory Receptor CellsBrainGanglia, SpinalAnimals, NewbornTrinucleotide Repeat ExpansionProtein Structure, TertiaryCatecholsPatch-Clamp TechniquesGABAergic NeuronsNeural InhibitionMice, Inbred C57BLModels, NeurologicalParkinson DiseaseProtein TransportCerebral CortexSignal TransductionAnimals, Genetically ModifiedFacial NerveModels, BiologicalHippocampusRecombinant Fusion ProteinsMembrane PotentialsTRPP Cation ChannelsTransfectionMotor Skills DisordersBlotting, WesternProteinsgamma-Aminobutyric AcidBrain Stem