Amyotrophic Lateral SclerosisSuperoxide DismutaseMotor Neuron DiseaseMotor NeuronsRNA-Binding Protein FUSDNA Repeat ExpansionSpinal CordGuamFrontotemporal DementiaRiluzoleInclusion BodiesFrontotemporal Lobar DegenerationMice, TransgenicNerve DegenerationMutationNeurodegenerative DiseasesDisease Models, AnimalFasciculationAnterior Horn CellsTDP-43 ProteinopathiesBulbar Palsy, ProgressiveNeurofilament ProteinsDisease ProgressionRats, TransgenicCycasMutation, MissenseAge of OnsetLithium CarbonateNeuroprotective AgentsDNA-Binding ProteinsExcitatory Amino Acid Transporter 2BrainAstrocytesMicrogliaMutant ProteinsPseudobulbar PalsyNeuronsRotarod Performance TestAmino Acid SubstitutionSialorrheaPyramidal TractsNoninvasive VentilationAxonal TransportRibonuclease, PancreaticAxonsNeuromuscular DiseasesAnimals, Genetically ModifiedAmino Acids, DiaminoPeripherinsMitochondriaMuscle WeaknessProtein FoldingCell DeathElectromyographyDementiaCopperCase-Control StudiesNeuromuscular JunctionLaughterPhenotypeNerve Tissue ProteinsNeurogliaParalysisParkinson DiseasePedigreeTracheostomyGlial Fibrillary Acidic ProteinCommunication Aids for DisabledItalyUbiquitinGlutamic AcidChromosomes, Human, Pair 9Muscular Atrophy, SpinalGliosisMuscle, SkeletalRespiratory InsufficiencyMotor CortexPyrazolonesOxidative StressMice, Inbred C57BLCentral Nervous SystemGlycine