Motor NeuronsNeuronsMotor Neuron DiseaseCell DifferentiationSurvival of Motor Neuron 1 ProteinNeurons, AfferentMotor CortexSurvival of Motor Neuron 2 ProteinEvoked Potentials, MotorSpinal CordAmyotrophic Lateral SclerosisCells, CulturedMuscular Atrophy, SpinalMotor ActivityNerve Tissue ProteinsAxonsGene Expression Regulation, DevelopmentalSMN Complex ProteinsAction PotentialsMice, TransgenicSignal TransductionImmunohistochemistryStem CellsTranscription FactorsMice, Inbred C57BLMolecular Motor ProteinsRNA, MessengerTime FactorsSynapsesElectric StimulationGene Expression RegulationNerve DegenerationCell LineNeuromuscular DiseasesGanglia, InvertebrateEmbryonic Stem CellsMice, KnockoutElectrophysiologyMolecular Sequence DataHomeodomain ProteinsMutationInterneuronsAnimals, NewbornCell LineageSynaptic TransmissionMovementCholinergic NeuronsDopaminergic NeuronsPhenotypeBrainAplysiaIn Situ HybridizationSuperoxide DismutaseSex DifferentiationNeuromuscular JunctionDendritesChick EmbryoDNA-Binding ProteinsSensory Receptor CellsDisease Models, AnimalElectromyographyAnimals, Genetically ModifiedEmbryo, MammalianGanglia, SpinalAnterior Horn CellsCell CountNeurogenesisGABAergic NeuronsGreen Fluorescent ProteinsPatch-Clamp TechniquesCell DivisionMuscle, SkeletalCell ProliferationCerebral CortexCell SurvivalNeural InhibitionBulbar Palsy, ProgressiveModels, NeurologicalGene ExpressionBase SequenceTretinoinReverse Transcriptase Polymerase Chain ReactionMusclesHippocampusCentral Nervous SystemNeuropeptidesMembrane PotentialsModels, BiologicalFacial Nervegamma-Aminobutyric AcidRats, Sprague-DawleyNeurofilament ProteinsNeuritesNeurogliaMotor Skills DisordersNerve Growth FactorsBrain StemCholine O-AcetyltransferaseBasic Helix-Loop-Helix Transcription FactorsZebrafish