Motor NeuronsNeuronsMotor Neuron DiseaseSurvival of Motor Neuron 1 ProteinNeurons, AfferentMotor CortexSurvival of Motor Neuron 2 ProteinEvoked Potentials, MotorSpinal CordAmyotrophic Lateral SclerosisCells, CulturedMuscular Atrophy, SpinalMotor ActivityAxonsCell LineNerve Tissue ProteinsAction PotentialsSMN Complex ProteinsCell DifferentiationImmunohistochemistryMolecular Sequence DataSignal TransductionMice, TransgenicElectric StimulationMolecular Motor ProteinsSynapsesElectrophysiologyRNA, MessengerTime FactorsGene Expression Regulation, DevelopmentalNerve DegenerationGene Expression RegulationGanglia, InvertebrateMutationNeuromuscular DiseasesBrainInterneuronsMice, Inbred C57BLSynaptic TransmissionBase SequenceTranscription FactorsGreen Fluorescent ProteinsPatch-Clamp TechniquesMovementAnimals, Genetically ModifiedAnimals, NewbornCholinergic NeuronsFibroblastsAplysiaDendritesDisease Models, AnimalDopaminergic NeuronsSuperoxide DismutaseModels, BiologicalGanglia, SpinalElectromyographyCell SurvivalNeuromuscular JunctionSensory Receptor CellsAnterior Horn CellsCell CountModels, NeurologicalGene ExpressionOrgan SpecificityChick EmbryoNeural InhibitionAmino Acid SequenceAstrocytesGABAergic NeuronsStem CellsNeurogliaBulbar Palsy, ProgressiveHippocampusTransfectionMice, KnockoutMembrane PotentialsCerebral CortexIn Situ HybridizationCentral Nervous SystemRats, Sprague-DawleyDNA-Binding ProteinsApoptosisTranscription, GeneticPhenotypeHomeodomain ProteinsNeuropeptidesEmbryo, MammalianFacial Nervegamma-Aminobutyric AcidMotor Skills DisordersRats, WistarCell DeathMuscle, SkeletalCalciumMicroscopy, FluorescenceHeLa CellsCell LineageBrain StemMicroscopy, ConfocalFluorescent Antibody Technique