CystinuriaAmino Acids, DiaminoAmino Acid Transport Systems, BasicCystineOrnithineOrnithine DecarboxylaseAmino AcidsAmino Acid Transport SystemsLysineArginineOrnithine CarbamoyltransferaseAmino Acid SequenceBiological TransportMolecular Sequence DataSequence Homology, Amino AcidOrnithine-Oxo-Acid TransaminaseOrnithine Carbamoyltransferase Deficiency DiseaseAmino Acid SubstitutionCloning, MolecularEflornithinePutrescineCarboxy-LyasesAmino Acids, EssentialBase SequenceKineticsSequence AlignmentCitrullineEscherichia coliSpermidineMutationAmino Acid MotifsBinding SitesMutagenesis, Site-DirectedDNA, ComplementarySequence Homology, Nucleic AcidTransaminasesLeucineDNARecombinant ProteinsBiogenic PolyaminesProtein ConformationAdenosylmethionine DecarboxylaseAmino Acids, AromaticPeptide FragmentsRNA, MessengerModels, MolecularAmino Acids, Branched-ChainProlineStructure-Activity RelationshipSpermineAmino Acids, SulfurSubstrate SpecificityMolecular WeightCell LineArginaseGyrate AtrophyBacterial ProteinsProteinsProtein Structure, TertiaryRestriction MappingGlutamineProtein BindingDiaminesPeptidesLiverCarbamyl PhosphateAlanineGenes, BacterialElectrophoresis, Polyacrylamide GelPhylogenySequence Analysis, DNARecombinant Fusion ProteinsPlasmids