Congenital HyperinsulinismHyperinsulinismSulfonylurea ReceptorsReceptors, DrugPotassium Channels, Inwardly RectifyingDiazoxideHypoglycemiaDiagnostic Techniques, EndocrineHyperammonemiaATP-Binding Cassette TransportersGlutamate DehydrogenasePancreatectomyInfant, NewbornInsulinInsulinomaKATP ChannelsInsulin AntibodiesSulfonylurea CompoundsBeckwith-Wiedemann SyndromePotassium Channels3-Hydroxyacyl CoA DehydrogenasesFocal AdhesionsCongenital Disorders of GlycosylationMutationCyclin-Dependent Kinase Inhibitor p57Chromosomes, Human, Pair 11Islets of LangerhansTolbutamideBlood GlucoseMutation, MissenseInsulin-Secreting CellsHyperandrogenismChlorthalidoneHamartomaPancreasOctreotideSyndromeHeterozygotePedigreeProinsulinDelayed DiagnosisSeizuresC-PeptidePancreatic NeoplasmsPrenatal DiagnosisEarly DiagnosisMosaicismHypopituitarismSensitivity and SpecificityGenes, DominantHomozygoteAmmoniaPhenotypeAdenosine TriphosphatePoint MutationGlucoseHyperplasiaRetrospective StudiesGlucose Tolerance TestTreatment OutcomeDiagnosisGlomerulosclerosis, Focal SegmentalDNA Mutational Analysis