Motor NeuronsMotor Neuron DiseaseNeuronsNerve DegenerationSurvival of Motor Neuron 1 ProteinRetinal DegenerationMacular DegenerationNeurons, AfferentCell SurvivalSurvival of Motor Neuron 2 ProteinMotor CortexAmyotrophic Lateral SclerosisSurvival RateEvoked Potentials, MotorSpinal CordWallerian DegenerationMuscular Atrophy, SpinalAxonsMotor ActivitySMN Complex ProteinsNerve Tissue ProteinsAction PotentialsTime FactorsDisease Models, AnimalImmunohistochemistryDisease-Free SurvivalMice, TransgenicCells, CulturedSurvivalIntervertebral Disc DegenerationSynapsesMolecular Motor ProteinsElectric StimulationNeuromuscular DiseasesMice, Inbred C57BLMutationBrainGanglia, InvertebrateSurvival AnalysisElectrophysiologyDopaminergic NeuronsSuperoxide DismutaseFrontotemporal Lobar DegenerationInterneuronsSynaptic TransmissionCholinergic NeuronsMovementGraft SurvivalAnimals, NewbornNeuromuscular JunctionAnterior Horn CellsAnimals, Genetically ModifiedDendritesGanglia, SpinalElectromyographyAplysiaSensory Receptor CellsMice, KnockoutCell CountCerebral CortexCell DeathSignal TransductionHippocampusPatch-Clamp TechniquesGABAergic NeuronsWet Macular DegenerationModels, NeurologicalAxonal TransportNeural InhibitionBulbar Palsy, ProgressiveApoptosisRats, Sprague-DawleyRetinaFacial NerveNeurofilament ProteinsGreen Fluorescent ProteinsMembrane PotentialsPhotoreceptor Cells, VertebrateBrain StemCentral Nervous SystemTreatment OutcomeMotor Skills DisordersAnalysis of VarianceNeural Conductiongamma-Aminobutyric AcidNerve Growth FactorsCell DifferentiationBehavior, AnimalCholine O-AcetyltransferaseNeuropeptidesMuscle, SkeletalNeurogliaDopamineAxotomyGene Expression Regulation, DevelopmentalCerebellumRetrograde DegenerationRats, WistarGangliaAstrocytes